Preferred Name

Progressive Supranuclear Palsy

Synonyms

Steele-Richardson-Olszewski Disease|Progressive Supranuclear Ophthalmoplegia|Steele-Richardson-Olszewski Syndrome

ID

http://bioontology.org/projects/ontologies/birnlex#birnlex_12697

abbrev

class_or_indiv

true

definition

A degenerative disease of the central nervous system characterized by balance difficulties; OCULAR MOTILITY DISORDERS (supranuclear ophthalmoplegia); DYSARTHRIA; swallowing difficulties; and axial DYSTONIA. Onset is usually in the fifth decade and disease progression occurs over several years. Pathologic findings include neurofibrillary degeneration and neuronal loss in the dorsal MESENCEPHALON; SUBTHALAMIC NUCLEUS; RED NUCLEUS; pallidum; dentate nucleus; and vestibular nuclei (MeSH).

external_id_urls

http://www.nlm.nih.gov/cgi/mesh/2008/MB_cgi?field=uid&term=D013494

external_ids

meshUID:D013494

label

Progressive Supranuclear Palsy

mod_date

2007-10-08

preferred_label

Progressive Supranuclear Palsy

prefixIRI

birnlex_12697

prefLabel

Progressive Supranuclear Palsy

retired

false

synonyms

Steele-Richardson-Olszewski Disease|Progressive Supranuclear Ophthalmoplegia|Steele-Richardson-Olszewski Syndrome

subClassOf

http://bioontology.org/projects/ontologies/birnlex#birnlex_12696

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