Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Adrenocortical carcinoma

Synonyms

ACC

Definitions

A rare cancer that arises from the adrenal cortex.

ID

http://www.orpha.net/ORDO/Orphanet_1501

alternative_term

ACC

definition

A rare cancer that arises from the adrenal cortex.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=1501

has_age_of_onset

Childhood

has_inheritance

Not applicable

hasDbXref

ICD-11:2D11.Z

MeSH:D018268

ICD-10:C74.0

OMIM:202300

UMLS:C0206686

MedDRA:10001388

label

Adrenocortical carcinoma

notation

ORPHA:1501

part_of

http://www.orpha.net/ORDO/Orphanet_100091

http://www.orpha.net/ORDO/Orphanet_314749

prefixIRI

ORDO:Orphanet_1501

prefLabel

Adrenocortical carcinoma

present_in

Estonia AND has_annual_incidence_average_value : 0.314 AND has_annual_incidence_range : 1-9 / 1 000 000

Czech Republic AND has_annual_incidence_average_value : 0.271 AND has_annual_incidence_range : 1-9 / 1 000 000

Europe AND has_point_prevalence_average_value : 0.75 AND has_point_prevalence_range : 1-9 / 1 000 000

Poland AND has_annual_incidence_average_value : 0.433 AND has_annual_incidence_range : 1-9 / 1 000 000

Belgium AND has_annual_incidence_average_value : 0.18 AND has_annual_incidence_range : 1-9 / 1 000 000

Italy AND has_annual_incidence_average_value : 0.288 AND has_annual_incidence_range : 1-9 / 1 000 000

Malta AND has_annual_incidence_average_value : 0.188 AND has_annual_incidence_range : 1-9 / 1 000 000

Slovakia AND has_annual_incidence_average_value : 0.234 AND has_annual_incidence_range : 1-9 / 1 000 000

Latvia AND has_annual_incidence_average_value : 0.514 AND has_annual_incidence_range : 1-9 / 1 000 000

Europe AND has_annual_incidence_average_value : 0.03 AND has_annual_incidence_range : <1 / 1 000 000

Spain AND has_annual_incidence_average_value : 0.215 AND has_annual_incidence_range : 1-9 / 1 000 000

United Kingdom AND has_annual_incidence_average_value : 0.183 AND has_annual_incidence_range : 1-9 / 1 000 000

Norway AND has_annual_incidence_average_value : 0.226 AND has_annual_incidence_range : 1-9 / 1 000 000

Switzerland AND has_annual_incidence_average_value : 0.141 AND has_annual_incidence_range : 1-9 / 1 000 000

Ireland AND has_annual_incidence_average_value : 0.133 AND has_annual_incidence_range : 1-9 / 1 000 000

Croatia AND has_annual_incidence_average_value : 0.547 AND has_annual_incidence_range : 1-9 / 1 000 000

Germany AND has_annual_incidence_average_value : 0.173 AND has_annual_incidence_range : 1-9 / 1 000 000

Bulgaria AND has_annual_incidence_average_value : 0.249 AND has_annual_incidence_range : 1-9 / 1 000 000

Netherlands AND has_annual_incidence_average_value : 0.167 AND has_annual_incidence_range : 1-9 / 1 000 000

Iceland AND has_annual_incidence_average_value : 0.17 AND has_annual_incidence_range : 1-9 / 1 000 000

Slovenia AND has_annual_incidence_average_value : 0.244 AND has_annual_incidence_range : 1-9 / 1 000 000

Austria AND has_annual_incidence_average_value : 0.173 AND has_annual_incidence_range : 1-9 / 1 000 000

Portugal AND has_annual_incidence_average_value : 0.082 AND has_annual_incidence_range : <1 / 1 000 000

Lithuania AND has_annual_incidence_average_value : 0.464 AND has_annual_incidence_range : 1-9 / 1 000 000

Finland AND has_annual_incidence_average_value : 0.225 AND has_annual_incidence_range : 1-9 / 1 000 000

treeView

http://www.orpha.net/ORDO/Orphanet_100091

http://www.orpha.net/ORDO/Orphanet_314749

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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Delete Mapping To Ontology Source
http://purl.obolibrary.org/obo/DOID_3948 DOID LOOM
http://purl.obolibrary.org/obo/DOID_3948 DOID LOOM
http://purl.obolibrary.org/obo/HP_0006744 HP LOOM
http://purl.bioontology.org/ontology/MESH/D018268 MESH LOOM
http://www.phoc.org.cn/pmo/class/PMO_00037938 PMAPP-PMO LOOM
http://purl.jp/bio/4/id/200906061244127997 IOBC LOOM
http://www.semanticweb.org/ontologies/2012/11/abnormalities.owl#phenodb:2455 IFAR LOOM
http://www.limics.org/hrdo/rdfns#pat_id_3731 HRDO LOOM
http://purl.bioontology.org/ontology/PDQ/CDR0000038758 PDQ LOOM
http://purl.obolibrary.org/obo/HP_0006744 UPHENO LOOM
http://id.nlm.nih.gov/mesh/D018268 MDM LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_3948 NATPRO LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU061374 OMIM LOOM
http://purl.obolibrary.org/obo/OMIT_0018500 OMIT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.470.200.025.152 RH-MESH LOOM
http://purl.bioontology.org/ontology/MEDDRA/10001388 MEDDRA LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C19.053.098.265.750 RH-MESH LOOM
http://www.gamuts.net/entity#adrenocortical_carcinoma GAMUTS LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.588.322.078.265.750 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C19.344.078.265.750 RH-MESH LOOM
http://identifiers.org/omim/202300 REXO LOOM
http://identifiers.org/omim/202300 GEXO LOOM
http://identifiers.org/omim/202300 RETO LOOM
http://purl.obolibrary.org/obo/OMIM_202300 CCO LOOM
http://purl.obolibrary.org/obo/DOID_3948 CLO LOOM
http://purl.obolibrary.org/obo/DOID_3948 DTO LOOM
http://purl.obolibrary.org/obo/DOID_3948 BAO LOOM
http://purl.obolibrary.org/obo/DOID_3948 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_3948 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_3948 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_3948 FNS-H LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D018268 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C19.053.347.500.750 RH-MESH LOOM
http://www.gamuts.net/entity#adrenocortical_carcinoma GAMUTS REST