Preferred Name

Motor Neuron Disease

Synonyms

Motor System Disease

ID

http://bioontology.org/projects/ontologies/birnlex#birnlex_12565

abbrev

class_or_indiv

true

definition

Diseases characterized by a selective degeneration of the motor neurons of the spinal cord, brainstem, or motor cortex. Clinical subtypes are distinguished by the major site of degeneration. In AMYOTROPHIC LATERAL SCLEROSIS there is involvement of upper, lower, and brainstem motor neurons. In progressive muscular atrophy and related syndromes (see MUSCULAR ATROPHY, SPINAL) the motor neurons in the spinal cord are primarily affected. With progressive bulbar palsy ( BULBAR PALSY, PROGRESSIVE), the initial degeneration occurs in the brainstem. In primary lateral sclerosis, the cortical neurons are affected in isolation (MeSH).

external_id_urls

http://www.nlm.nih.gov/cgi/mesh/2008/MB_cgi?field=uid&term=D016472

external_ids

umlsCUI:C0085084|meshUID:D016472

label

Motor Neuron Disease

mod_date

2007-11-18

preferred_label

Motor Neuron Disease

prefixIRI

birnlex_12565

prefLabel

Motor Neuron Disease

retired

false

synonyms

Motor System Disease

subClassOf

http://bioontology.org/projects/ontologies/birnlex#birnlex_2086

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