loading...| Preferred Name |
Double outlet right ventricle |
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| Synonyms |
Double-outlet right ventricle DORV |
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| Definitions |
During the development of the heart, the outflow tract initially connects exclusively with the primitive right ventricle and must undergo extensive remodelling to divide into a separate pulmonary artery and aorta; subsequently, there is continued remodelling to establish direct continuity from the left ventricle to the aorta. DORV encompasses a wide spectrum of anatomic arrangements and pathophysiologic disturbances. At one end of the spectrum, it mimics tetralogy of Fallot in the presence of pulmonary stenosis, or a large ventricular septal defect (VSD) in the absence of such stenosis. At the other end of the spectrum, it behaves like transposition of the great arteries with a VSD. Double outlet right ventricle (DORV) is a type of ventriculoarterial connection in which both great vessels arise entirely or predominantly from the right ventricle. |
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| ID |
http://purl.obolibrary.org/obo/HP_0001719 |
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| comment |
During the development of the heart, the outflow tract initially connects exclusively with the primitive right ventricle and must undergo extensive remodelling to divide into a separate pulmonary artery and aorta; subsequently, there is continued remodelling to establish direct continuity from the left ventricle to the aorta. DORV encompasses a wide spectrum of anatomic arrangements and pathophysiologic disturbances. At one end of the spectrum, it mimics tetralogy of Fallot in the presence of pulmonary stenosis, or a large ventricular septal defect (VSD) in the absence of such stenosis. At the other end of the spectrum, it behaves like transposition of the great arteries with a VSD. |
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| database_cross_reference |
SNOMEDCT_US:7484005 UMLS:C0013069 MSH:D004310 Fyler:600 Fyler:606 |
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| definition |
Double outlet right ventricle (DORV) is a type of ventriculoarterial connection in which both great vessels arise entirely or predominantly from the right ventricle. |
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| equivalentClass | ||
| has exact synonym |
Double-outlet right ventricle DORV |
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| id |
HP:0001719 |
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| label |
Double outlet right ventricle |
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| notation |
HP:0001719 |
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| prefLabel |
Double outlet right ventricle |
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| subClassOf |
http://purl.obolibrary.org/obo/MP_0010426 |