Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Polyarteritis nodosa

Synonyms

Periarteritis nodosa

Definitions

A rare, clinically heterogeneous, systemic disease characterized by necrotizing inflammatory lesions affecting medium-sized blood vessels. It most commonly affects skin, joints, peripheral nerves and the gastrointestinal tract.

ID

http://www.orpha.net/ORDO/Orphanet_767

alternative_term

Periarteritis nodosa

PAN

Küssmaul-Maier disease

definition

A rare, clinically heterogeneous, systemic disease characterized by necrotizing inflammatory lesions affecting medium-sized blood vessels. It most commonly affects skin, joints, peripheral nerves and the gastrointestinal tract.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=767

has_age_of_onset

All ages

has_inheritance

Not applicable

hasDbXref

ICD-11:4A44.4

UMLS:C0031036

MeSH:D010488

MedDRA:10036024

ICD-10:M30.0

label

Polyarteritis nodosa

notation

ORPHA:767

part_of

http://www.orpha.net/ORDO/Orphanet_156143

http://www.orpha.net/ORDO/Orphanet_567560

http://www.orpha.net/ORDO/Orphanet_209007

prefixIRI

ORDO:Orphanet_767

prefLabel

Polyarteritis nodosa

present_in

Australia AND has_annual_incidence_average_value : 0.11 AND has_annual_incidence_range : 1-9 / 1 000 000

France AND has_point_prevalence_average_value : 3.07 AND has_point_prevalence_range : 1-9 / 100 000

Sweden AND has_point_prevalence_average_value : 3.1 AND has_point_prevalence_range : 1-9 / 100 000

Europe AND has_point_prevalence_average_value : 3.16 AND has_point_prevalence_range : 1-9 / 100 000

Norway AND has_point_prevalence_average_value : 3.3 AND has_point_prevalence_range : 1-9 / 100 000

Norway AND has_annual_incidence_average_value : 0.05 AND has_annual_incidence_range : <1 / 1 000 000

United Kingdom AND has_annual_incidence_average_value : 0.9 AND has_annual_incidence_range : 1-9 / 1 000 000

Spain AND has_annual_incidence_average_value : 0.62 AND has_annual_incidence_range : 1-9 / 1 000 000

Germany AND has_annual_incidence_average_value : 0.04 AND has_annual_incidence_range : <1 / 1 000 000

treeView

http://www.orpha.net/ORDO/Orphanet_156143

http://www.orpha.net/ORDO/Orphanet_567560

http://www.orpha.net/ORDO/Orphanet_209007

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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Delete Mapping To Ontology Source
http://www.ebi.ac.uk/efo/EFO_0009012 EFO LOOM
http://purl.obolibrary.org/obo/MONDO_0019170 MONDO LOOM
http://purl.obolibrary.org/obo/MONDO_0019170 EFO LOOM
http://purl.bioontology.org/ontology/ICD10/M30.0 ICD10 LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C17.800.862.625 RH-MESH LOOM
http://purl.obolibrary.org/obo/DOID_9810 DOID LOOM
http://purl.obolibrary.org/obo/DOID_9810 BAO LOOM
http://purl.obolibrary.org/obo/DOID_9810 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_9810 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_9810 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_9810 FNS-H LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Polyarteritis_Nodosa CSEO LOOM
http://www.ebi.ac.uk/efo/EFO_0009012 EFO LOOM
http://purl.obolibrary.org/obo/OMIT_0011481 OMIT LOOM
http://purl.bioontology.org/ontology/RCTV2/G750.00 RCTV2 LOOM
http://purl.bioontology.org/ontology/AIR/PAN AI-RHEUM LOOM
http://identifiers.org/omim/615688 REXO LOOM
http://identifiers.org/omim/615688 GEXO LOOM
http://identifiers.org/omim/615688 RETO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#9483 OCHV LOOM
http://www.gamuts.net/entity#polyarteritis_nodosa GAMUTS LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU044973 OMIM LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/155441006 SNOMEDCT LOOM
http://purl.bioontology.org/ontology/AIR/DXPAN AI-RHEUM LOOM
http://www.co-ode.org/ontologies/galen#PolyarteritisNodosa GALEN LOOM
http://purl.bioontology.org/ontology/WHO/0083 WHO-ART LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C14.907.940.090.720 RH-MESH LOOM
http://www.phoc.org.cn/pmo/class/PMO_00036413 PMAPP-PMO LOOM
http://purl.bioontology.org/ontology/MEDDRA/10036024 MEDDRA LOOM
http://purl.bioontology.org/ontology/RCD/XE0VU RCD LOOM
http://purl.obolibrary.org/obo/MPATH_756 MPATH LOOM
https://github.com/sap218/ocimido/blob/master/ontology/ocimido.owl#OCIMIDO_00071 OCIMIDO LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C26847 NCIT LOOM
http://purl.obolibrary.org/obo/DERMO_0003231 DERMO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C14.907.184.595 RH-MESH LOOM
http://purl.bioontology.org/ontology/ICD9CM/446.0 ICD9CM LOOM
http://purl.obolibrary.org/obo/MONDO_0019170 EFO LOOM
http://purl.obolibrary.org/obo/MONDO_0019170 DOVES LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C14.907.940.897.500 RH-MESH LOOM
http://www.owl-ontologies.com/unnamed.owl#RID19122 DERMLEX LOOM
http://purl.bioontology.org/ontology/MESH/D010488 MESH LOOM
http://purl.bioontology.org/ontology/CST/POLYARTERITIS%20NODOSA COSTART LOOM
http://purl.bioontology.org/ontology/SNMI/D3-81630 SNMI LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_9810 NATPRO LOOM
http://www.semanticweb.org/ontologies/STO.owl#OWLClass_7d678e75_4a34_464c_af93_c84660e6df9b STO-DRAFT LOOM
http://www.semanticweb.org/ontologies/STO.owl#OWLClass_7d678e75_4a34_464c_af93_c84660e6df9b CVAO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0031036 OCHV LOOM
http://purl.bioontology.org/ontology/ICD10CM/M30.0 ICD10CM LOOM
http://purl.bioontology.org/ontology/ICPC2P/K99024 ICPC2P LOOM
http://nanbyodata.jp/ontology/NANDO_1200261 NANDO LOOM
http://www.ustb.edu.cn/thesauri/tocr/v1/data#C571345044435366010 ACVD_ONTOLOGY LOOM
http://www.limics.org/hrdo/rdfns#pat_id_3403 HRDO LOOM
http://radlex.org/RID/RID3692 RADLEX LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D010488 RH-MESH LOOM
http://purl.obolibrary.org/obo/NCIT_C26847 BERO LOOM
http://www.gamuts.net/entity#polyarteritis_nodosa GAMUTS REST