Preferred Name |
Polyarteritis nodosa |
|
Synonyms |
Periarteritis nodosa |
|
Definitions |
A rare, clinically heterogeneous, systemic disease characterized by necrotizing inflammatory lesions affecting medium-sized blood vessels. It most commonly affects skin, joints, peripheral nerves and the gastrointestinal tract. |
|
ID |
http://www.orpha.net/ORDO/Orphanet_767 |
|
alternative_term |
Periarteritis nodosa PAN Küssmaul-Maier disease |
|
definition |
A rare, clinically heterogeneous, systemic disease characterized by necrotizing inflammatory lesions affecting medium-sized blood vessels. It most commonly affects skin, joints, peripheral nerves and the gastrointestinal tract. |
|
definition_citation |
Orphanet |
|
expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=767 |
|
has_age_of_onset |
All ages |
|
has_inheritance |
Not applicable |
|
hasDbXref |
ICD-11:4A44.4 UMLS:C0031036 MeSH:D010488 MedDRA:10036024 ICD-10:M30.0 |
|
label |
Polyarteritis nodosa |
|
notation |
ORPHA:767 |
|
part_of |
http://www.orpha.net/ORDO/Orphanet_156143 |
|
prefixIRI |
ORDO:Orphanet_767 |
|
prefLabel |
Polyarteritis nodosa |
|
present_in |
Australia AND has_annual_incidence_average_value : 0.11 AND has_annual_incidence_range : 1-9 / 1 000 000 France AND has_point_prevalence_average_value : 3.07 AND has_point_prevalence_range : 1-9 / 100 000 Sweden AND has_point_prevalence_average_value : 3.1 AND has_point_prevalence_range : 1-9 / 100 000 Europe AND has_point_prevalence_average_value : 3.16 AND has_point_prevalence_range : 1-9 / 100 000 Norway AND has_point_prevalence_average_value : 3.3 AND has_point_prevalence_range : 1-9 / 100 000 Norway AND has_annual_incidence_average_value : 0.05 AND has_annual_incidence_range : <1 / 1 000 000 United Kingdom AND has_annual_incidence_average_value : 0.9 AND has_annual_incidence_range : 1-9 / 1 000 000 Spain AND has_annual_incidence_average_value : 0.62 AND has_annual_incidence_range : 1-9 / 1 000 000 Germany AND has_annual_incidence_average_value : 0.04 AND has_annual_incidence_range : <1 / 1 000 000 |
|
treeView |
http://www.orpha.net/ORDO/Orphanet_156143 |
|
subClassOf |