Preferred Name |
Kaposi sarcoma |
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Synonyms |
|
|
Definitions |
A rare vascular tumor that is characterized by human herpes virus 8 (HHV-8)-induced endothelial inflammatory neoplasm that develops with various clinically distinct settings, manifesting mostly as cutaneous lesions, or mucosal or visceral involvement. |
|
ID |
http://www.orpha.net/ORDO/Orphanet_33276 |
|
definition |
A rare vascular tumor that is characterized by human herpes virus 8 (HHV-8)-induced endothelial inflammatory neoplasm that develops with various clinically distinct settings, manifesting mostly as cutaneous lesions, or mucosal or visceral involvement. |
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definition_citation |
Orphanet |
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expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=33276 |
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has_age_of_onset |
Adult |
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has_inheritance |
Not applicable |
|
hasDbXref |
MedDRA:10023284 ICD-10:C46.2 ICD-10:C46.9 OMIM:148000 ICD-11:1C61.30 ICD-10:C46.1 ICD-10:C46.7 ICD-10:C46.0 ICD-11:XH36A5 ICD-11:1C60.30 ICD-11:2B57.1 ICD-10:C46.8 ICD-10:C46.3 MeSH:D012514 ICD-11:2B57.2 ICD-11:2B57.Y ICD-11:2B57.0 ICD-11:2B57 UMLS:C0036220 |
|
label |
Kaposi sarcoma |
|
notation |
ORPHA:33276 |
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part_of |
http://www.orpha.net/ORDO/Orphanet_3394 |
|
prefixIRI |
ORDO:Orphanet_33276 |
|
prefLabel |
Kaposi sarcoma |
|
present_in |
Slovakia AND has_annual_incidence_average_value : 0.05 AND has_annual_incidence_range : <1 / 1 000 000 Europe AND has_lifetime_prevalence_average_value : 2.11 AND has_lifetime_prevalence_range : 1-9 / 100 000 Croatia AND has_annual_incidence_average_value : 0.133 AND has_annual_incidence_range : 1-9 / 1 000 000 Austria AND has_annual_incidence_average_value : 0.051 AND has_annual_incidence_range : <1 / 1 000 000 Slovenia AND has_annual_incidence_average_value : 0.056 AND has_annual_incidence_range : <1 / 1 000 000 Europe AND has_point_prevalence_range : 1-9 / 100 000 Italy AND has_annual_incidence_average_value : 1.142 AND has_annual_incidence_range : 1-9 / 100 000 Ireland AND has_annual_incidence_average_value : 0.111 AND has_annual_incidence_range : 1-9 / 1 000 000 Poland AND has_annual_incidence_average_value : 0.043 AND has_annual_incidence_range : <1 / 1 000 000 Spain AND has_annual_incidence_average_value : 0.546 AND has_annual_incidence_range : 1-9 / 1 000 000 Portugal AND has_annual_incidence_average_value : 0.915 AND has_annual_incidence_range : 1-9 / 1 000 000 Iceland AND has_annual_incidence_average_value : 1.363 AND has_annual_incidence_range : 1-9 / 100 000 Europe AND has_annual_incidence_average_value : 0.34 AND has_annual_incidence_range : 1-9 / 1 000 000 Switzerland AND has_annual_incidence_average_value : 0.163 AND has_annual_incidence_range : 1-9 / 1 000 000 Norway AND has_annual_incidence_average_value : 0.027 AND has_annual_incidence_range : <1 / 1 000 000 Bulgaria AND has_annual_incidence_average_value : 0.099 AND has_annual_incidence_range : <1 / 1 000 000 Lithuania AND has_annual_incidence_average_value : 0.112 AND has_annual_incidence_range : 1-9 / 1 000 000 Netherlands AND has_annual_incidence_average_value : 0.278 AND has_annual_incidence_range : 1-9 / 1 000 000 Latvia AND has_annual_incidence_average_value : 0.108 AND has_annual_incidence_range : 1-9 / 1 000 000 United Kingdom AND has_annual_incidence_average_value : 0.192 AND has_annual_incidence_range : 1-9 / 1 000 000 Estonia AND has_annual_incidence_average_value : 0.065 AND has_annual_incidence_range : <1 / 1 000 000 Czech Republic AND has_annual_incidence_average_value : 0.092 AND has_annual_incidence_range : <1 / 1 000 000 Belgium AND has_annual_incidence_average_value : 0.075 AND has_annual_incidence_range : <1 / 1 000 000 Germany AND has_annual_incidence_average_value : 0.076 AND has_annual_incidence_range : <1 / 1 000 000 Finland AND has_annual_incidence_average_value : 0.014 AND has_annual_incidence_range : <1 / 1 000 000 Malta AND has_annual_incidence_average_value : 0.597 AND has_annual_incidence_range : 1-9 / 1 000 000 |
|
treeView |
http://www.orpha.net/ORDO/Orphanet_3394 |
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subClassOf |