Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Kaposi sarcoma

Synonyms
Definitions

A rare vascular tumor that is characterized by human herpes virus 8 (HHV-8)-induced endothelial inflammatory neoplasm that develops with various clinically distinct settings, manifesting mostly as cutaneous lesions, or mucosal or visceral involvement.

ID

http://www.orpha.net/ORDO/Orphanet_33276

definition

A rare vascular tumor that is characterized by human herpes virus 8 (HHV-8)-induced endothelial inflammatory neoplasm that develops with various clinically distinct settings, manifesting mostly as cutaneous lesions, or mucosal or visceral involvement.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=33276

has_age_of_onset

Adult

has_inheritance

Not applicable

hasDbXref

MedDRA:10023284

ICD-10:C46.2

ICD-10:C46.9

OMIM:148000

ICD-11:1C61.30

ICD-10:C46.1

ICD-10:C46.7

ICD-10:C46.0

ICD-11:XH36A5

ICD-11:1C60.30

ICD-11:2B57.1 

ICD-10:C46.8

ICD-10:C46.3

MeSH:D012514

ICD-11:2B57.2

ICD-11:2B57.Y

ICD-11:2B57.0

ICD-11:2B57

UMLS:C0036220

label

Kaposi sarcoma

notation

ORPHA:33276

part_of

http://www.orpha.net/ORDO/Orphanet_3394

http://www.orpha.net/ORDO/Orphanet_102024

http://www.orpha.net/ORDO/Orphanet_211237

prefixIRI

ORDO:Orphanet_33276

prefLabel

Kaposi sarcoma

present_in

Slovakia AND has_annual_incidence_average_value : 0.05 AND has_annual_incidence_range : <1 / 1 000 000

Europe AND has_lifetime_prevalence_average_value : 2.11 AND has_lifetime_prevalence_range : 1-9 / 100 000

Croatia AND has_annual_incidence_average_value : 0.133 AND has_annual_incidence_range : 1-9 / 1 000 000

Austria AND has_annual_incidence_average_value : 0.051 AND has_annual_incidence_range : <1 / 1 000 000

Slovenia AND has_annual_incidence_average_value : 0.056 AND has_annual_incidence_range : <1 / 1 000 000

Europe AND has_point_prevalence_range : 1-9 / 100 000

Italy AND has_annual_incidence_average_value : 1.142 AND has_annual_incidence_range : 1-9 / 100 000

Ireland AND has_annual_incidence_average_value : 0.111 AND has_annual_incidence_range : 1-9 / 1 000 000

Poland AND has_annual_incidence_average_value : 0.043 AND has_annual_incidence_range : <1 / 1 000 000

Spain AND has_annual_incidence_average_value : 0.546 AND has_annual_incidence_range : 1-9 / 1 000 000

Portugal AND has_annual_incidence_average_value : 0.915 AND has_annual_incidence_range : 1-9 / 1 000 000

Iceland AND has_annual_incidence_average_value : 1.363 AND has_annual_incidence_range : 1-9 / 100 000

Europe AND has_annual_incidence_average_value : 0.34 AND has_annual_incidence_range : 1-9 / 1 000 000

Switzerland AND has_annual_incidence_average_value : 0.163 AND has_annual_incidence_range : 1-9 / 1 000 000

Norway AND has_annual_incidence_average_value : 0.027 AND has_annual_incidence_range : <1 / 1 000 000

Bulgaria AND has_annual_incidence_average_value : 0.099 AND has_annual_incidence_range : <1 / 1 000 000

Lithuania AND has_annual_incidence_average_value : 0.112 AND has_annual_incidence_range : 1-9 / 1 000 000

Netherlands AND has_annual_incidence_average_value : 0.278 AND has_annual_incidence_range : 1-9 / 1 000 000

Latvia AND has_annual_incidence_average_value : 0.108 AND has_annual_incidence_range : 1-9 / 1 000 000

United Kingdom AND has_annual_incidence_average_value : 0.192 AND has_annual_incidence_range : 1-9 / 1 000 000

Estonia AND has_annual_incidence_average_value : 0.065 AND has_annual_incidence_range : <1 / 1 000 000

Czech Republic AND has_annual_incidence_average_value : 0.092 AND has_annual_incidence_range : <1 / 1 000 000

Belgium AND has_annual_incidence_average_value : 0.075 AND has_annual_incidence_range : <1 / 1 000 000

Germany AND has_annual_incidence_average_value : 0.076 AND has_annual_incidence_range : <1 / 1 000 000

Finland AND has_annual_incidence_average_value : 0.014 AND has_annual_incidence_range : <1 / 1 000 000

Malta AND has_annual_incidence_average_value : 0.597 AND has_annual_incidence_range : 1-9 / 1 000 000

treeView

http://www.orpha.net/ORDO/Orphanet_3394

http://www.orpha.net/ORDO/Orphanet_102024

http://www.orpha.net/ORDO/Orphanet_211237

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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