National Cancer Institute Thesaurus

Last uploaded: February 23, 2024
Preferred Name

Polyostotic Fibrous Dysplasia

Synonyms

Polyostotic Fibrous Dysplasia

Polyostotic Fibrous Dysplasia of Bone

Definitions

Fibrous dysplasia affecting more than one bone. When it is associated with café-au-lait skin pigmentation and endocrine disorders, it is known as McCune-Albright syndrome.

ID

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C34610

code

C34610

Concept_In_Subset

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C90259

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C99147

Contributing_Source

NICHD

DEFINITION

Fibrous dysplasia affecting more than one bone. When it is associated with café-au-lait skin pigmentation and endocrine disorders, it is known as McCune-Albright syndrome.

FULL_SYN

Polyostotic Fibrous Dysplasia

Polyostotic Fibrous Dysplasia of Bone

label

Polyostotic Fibrous Dysplasia

Legacy Concept Name

Polyostotic_Fibrous_Dysplasia_of_Bone

Neoplastic_Status

Benign

Preferred_Name

Polyostotic Fibrous Dysplasia

prefixIRI

Thesaurus:C34610

Semantic_Type

Neoplastic Process

UMLS_CUI

C0016065

subClassOf

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C34609

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