Preferred Name |
Polyostotic Fibrous Dysplasia |
|
Synonyms |
Polyostotic Fibrous Dysplasia Polyostotic Fibrous Dysplasia of Bone |
|
Definitions |
Fibrous dysplasia affecting more than one bone. When it is associated with café-au-lait skin pigmentation and endocrine disorders, it is known as McCune-Albright syndrome. |
|
ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C34610 |
|
code |
C34610 |
|
Concept_In_Subset | ||
Contributing_Source |
NICHD |
|
DEFINITION |
Fibrous dysplasia affecting more than one bone. When it is associated with café-au-lait skin pigmentation and endocrine disorders, it is known as McCune-Albright syndrome. |
|
FULL_SYN |
Polyostotic Fibrous Dysplasia Polyostotic Fibrous Dysplasia of Bone |
|
label |
Polyostotic Fibrous Dysplasia |
|
Legacy Concept Name |
Polyostotic_Fibrous_Dysplasia_of_Bone |
|
Neoplastic_Status |
Benign |
|
Preferred_Name |
Polyostotic Fibrous Dysplasia |
|
prefixIRI |
Thesaurus:C34610 |
|
Semantic_Type |
Neoplastic Process |
|
UMLS_CUI |
C0016065 |
|
subClassOf |
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