Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Pulmonary Atresia

Synonyms

Atresia, Pulmonary Valve

Definitions

A congenital heart defect characterized by the narrowing or complete absence of the opening between the RIGHT VENTRICLE and the PULMONARY ARTERY. Lacking a normal PULMONARY VALVE, unoxygenated blood in the right ventricle can not be effectively pumped into the lung for oxygenation. Clinical features include rapid breathing, CYANOSIS, right ventricle atrophy, and abnormal heart sounds (HEART MURMURS).

ID

http://purl.bioontology.org/ontology/MESH/D018633

altLabel

Atresia, Pulmonary Valve

Pulmonary Valve Atresias

Atresia, Pulmonary

Valve Atresia, Pulmonary

Pulmonary Valve Atresia

Atresias, Pulmonary

Atresias, Pulmonary Valve

Valve Atresias, Pulmonary

Pulmonary Atresias

AQL

BL CF CI CL CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI

cui

C0242855

DC

1

definition

A congenital heart defect characterized by the narrowing or complete absence of the opening between the RIGHT VENTRICLE and the PULMONARY ARTERY. Lacking a normal PULMONARY VALVE, unoxygenated blood in the right ventricle can not be effectively pumped into the lung for oxygenation. Clinical features include rapid breathing, CYANOSIS, right ventricle atrophy, and abnormal heart sounds (HEART MURMURS).

DX

19950101

HN

95

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Machine permutation

95

Mapped from

http://purl.bioontology.org/ontology/MESH/C562833

http://purl.bioontology.org/ontology/MESH/C562832

MDA

19940523

MMR

20070709

MN

C16.131.240.850.906

C14.280.484.640

C14.240.850.937

notation

D018633

prefLabel

Pulmonary Atresia

TERMUI

T055492

T055494

T055488

T055490

T055489

T055495

T055491

T055493

TH

NLM (1995)

tui

T047

subClassOf

http://purl.bioontology.org/ontology/MESH/D054079

http://purl.bioontology.org/ontology/MESH/D006349

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/SNMI/D4-31610 SNMI CUI
http://purl.bioontology.org/ontology/MEDDRA/10052644 MEDDRA CUI
http://purl.bioontology.org/ontology/MDRFRE/10052644 MDRFRE CUI
http://purl.bioontology.org/ontology/ICD9CM/746.01 ICD9CM CUI
http://purl.bioontology.org/ontology/MDRFRE/10003653 MDRFRE CUI
http://purl.bioontology.org/ontology/OMIM/MTHU065495 OMIM CUI
http://purl.bioontology.org/ontology/ICPC2P/K73002 ICPC2P CUI
http://purl.bioontology.org/ontology/RCD/X77zV RCD CUI
http://purl.bioontology.org/ontology/MDRGER/10003653 MDRGER CUI
http://purl.bioontology.org/ontology/SCTSPA/204342004 SCTSPA CUI
http://purl.bioontology.org/ontology/SCTSPA/719955006 SCTSPA CUI
http://purl.bioontology.org/ontology/NDFRT/N0000003840 NDFRT CUI
http://purl.bioontology.org/ontology/ICD10CM/Q22.0 ICD10CM CUI
http://purl.bioontology.org/ontology/ICD10/Q22.0 ICD10 CUI
http://purl.bioontology.org/ontology/SNOMEDCT/204342004 SNOMEDCT CUI
http://purl.bioontology.org/ontology/SNOMEDCT/719955006 SNOMEDCT CUI
http://purl.bioontology.org/ontology/OMIM/MTHU004094 OMIM CUI
http://purl.bioontology.org/ontology/MSHFRE/D018633 MSHFRE CUI
http://purl.bioontology.org/ontology/MDRGER/10052644 MDRGER CUI
http://purl.bioontology.org/ontology/MEDDRA/10003653 MEDDRA CUI
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D018633 RH-MESH LOOM
http://purl.jp/bio/4/id/200906016075031696 IOBC LOOM
http://purl.obolibrary.org/obo/OMIT_0018810 OMIT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C14.280.484.640 RH-MESH LOOM
http://homes.esat.kuleuven.be/~bioiuser/chdwiki/index.php/CHDEPCC:090511 CHD LOOM
http://purl.bioontology.org/ontology/ICPC2P/K73002 ICPC2P LOOM
http://nanbyodata.jp/ontology/NANDO_2100074 NANDO LOOM
http://id.nlm.nih.gov/mesh/D018633 MDM LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C14.240.850.937 RH-MESH LOOM
http://www.phoc.org.cn/pmo/class/PMO_00040074 PMAPP-PMO LOOM
http://www.co-ode.org/ontologies/galen#PulmonaryAtresia GALEN LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU004094 OMIM LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C16.131.240.850.906 RH-MESH LOOM
http://www.gamuts.net/entity#pulmonary_atresia GAMUTS LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0242855 OCHV LOOM