Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Lymphangioleiomyomatosis

Synonyms

Lymphangiomyomatosis

Definitions

A disease characterized by the progressive invasion of SMOOTH MUSCLE CELLS into the LYMPHATIC VESSELS, and the BLOOD VESSELS. The majority of the cases occur in the LUNGS of women of child-bearing age, eventually blocking the flow of air, blood, and lymph. The common symptom is shortness of breath (DYSPNEA).

ID

http://purl.bioontology.org/ontology/MESH/D018192

altLabel

Lymphangiomyomatosis

Lymphangiomyomatoses

Lymphangioleiomyomatoses

AN

differentiate from LYMPHANGIOMYOMA; coordinate IM with precoordinated organ/neoplasm terms (IM) if relevant

AQL

BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI

cui

C0751674

DC

1

definition

A disease characterized by the progressive invasion of SMOOTH MUSCLE CELLS into the LYMPHATIC VESSELS, and the BLOOD VESSELS. The majority of the cases occur in the LUNGS of women of child-bearing age, eventually blocking the flow of air, blood, and lymph. The common symptom is shortness of breath (DYSPNEA).

DX

19940101

HN

2006 (1994)

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Machine permutation

2006; see LYMPHANGIOMYOMATOSIS 1994-2005

MDA

19930624

MMR

20180629

MN

C04.557.375.460.465

C15.604.515.562.465

C20.683.515.710.465

C04.557.450.692.500

notation

D018192

prefLabel

Lymphangioleiomyomatosis

TERMUI

T366603

T054450

TH

OMIM (2013)

NLM (2000)

NLM (1994)

GHR (2014)

ORD (2010)

tui

T191

subClassOf

http://purl.bioontology.org/ontology/MESH/D008203

http://purl.bioontology.org/ontology/MESH/D054973

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/ICD9CM/516.4 ICD9CM CUI
http://purl.bioontology.org/ontology/OMIM/606690 OMIM CUI
http://purl.bioontology.org/ontology/OMIM/605284 OMIM CUI
http://purl.bioontology.org/ontology/MDRGER/10049459 MDRGER CUI
http://purl.bioontology.org/ontology/MEDDRA/10049462 MEDDRA CUI
http://purl.bioontology.org/ontology/MDRGER/10049462 MDRGER CUI
http://purl.bioontology.org/ontology/RCD/BBU6. RCD CUI
http://purl.bioontology.org/ontology/NDFRT/N0000171692 NDFRT CUI
http://purl.bioontology.org/ontology/PDQ/CDR0000532373 PDQ CUI
http://purl.bioontology.org/ontology/CSP/4009-0064 CRISP CUI
http://purl.bioontology.org/ontology/MDRFRE/10049459 MDRFRE CUI
http://purl.bioontology.org/ontology/SCTSPA/73017001 SCTSPA CUI
http://purl.bioontology.org/ontology/MSHFRE/D018192 MSHFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10049459 MEDDRA CUI
http://purl.bioontology.org/ontology/SNMI/M-91741 SNMI CUI
http://purl.bioontology.org/ontology/MDRFRE/10049462 MDRFRE CUI
http://purl.bioontology.org/ontology/SNOMEDCT/73017001 SNOMEDCT CUI
http://purl.bioontology.org/ontology/ICD10CM/J84.81 ICD10CM CUI
http://purl.obolibrary.org/obo/MONDO_0011705 MONDO LOOM
http://purl.obolibrary.org/obo/MONDO_0011705 EFO LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Lymphangiomyomatosis CSEO LOOM
http://purl.bioontology.org/ontology/ICD9CM/516.4 ICD9CM LOOM
http://purl.bioontology.org/ontology/OMIM/606690 OMIM LOOM
http://www.orpha.net/ORDO/Orphanet_538 ORDO LOOM
http://identifiers.org/omim/606690 REXO LOOM
http://identifiers.org/omim/606690 GEXO LOOM
http://identifiers.org/omim/606690 RETO LOOM
http://purl.obolibrary.org/obo/OMIM_606690 CCO LOOM
http://purl.obolibrary.org/obo/NCIT_C3725 BERO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.375.460.465 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.450.692.500 RH-MESH LOOM
http://purl.obolibrary.org/obo/MONDO_0011705 DOVES LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_3319 NATPRO LOOM
http://www.owl-ontologies.com/unnamed.owl#RID19064 DERMLEX LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C15.604.515.562.465 RH-MESH LOOM
http://purl.obolibrary.org/obo/DOID_3319 DTO LOOM
http://purl.obolibrary.org/obo/DOID_3319 DOID LOOM
http://purl.obolibrary.org/obo/DOID_3319 BAO LOOM
http://purl.obolibrary.org/obo/DOID_3319 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_3319 ODAE LOOM
http://purl.obolibrary.org/obo/DOID_3319 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_3319 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_3319 FNS-H LOOM
http://purl.obolibrary.org/obo/OMIT_0018425 OMIT LOOM
http://nanbyodata.jp/ontology/NANDO_1200430 NANDO LOOM
http://purl.jp/bio/4/id/200906041280922069 IOBC LOOM
http://purl.bioontology.org/ontology/PDQ/CDR0000532373 PDQ LOOM
http://purl.bioontology.org/ontology/CSP/4009-0064 CRISP LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3725 NCIT LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#48475 OCHV LOOM
http://radlex.org/RID/RID4372 RADLEX LOOM
http://id.nlm.nih.gov/mesh/D018192 MDM LOOM
http://www.phoc.org.cn/pmo/class/PMO_00037882 PMAPP-PMO LOOM
http://purl.bioontology.org/ontology/MEDDRA/10049459 MEDDRA LOOM
http://www.gamuts.net/entity#lymphangioleiomyomatosis GAMUTS LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D018192 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C20.683.515.710.465 RH-MESH LOOM
http://www.limics.org/hrdo/rdfns#pat_id_3386 HRDO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0751674 OCHV LOOM
http://purl.bioontology.org/ontology/ICD10CM/J84.81 ICD10CM LOOM