An anomalous pulmonary venous return in which the right PULMONARY VEIN is not connected to the LEFT ATRIUM but to the INFERIOR VENA CAVA. Scimitar syndrome is named for the crescent- or Turkish sword-like shadow in the chest radiography and is often associated with hypoplasia of the right lung and right pulmonary artery, and dextroposition of the heart.
ID
http://purl.bioontology.org/ontology/MESH/D012587
altLabel
TAPVR1
Scimitar Anomaly
Anomalous Pulmonary Venous Return
Pulmonary Venous Return Anomaly
Anomaly, Scimitar
Total Anomalous Pulmonary Venous Return
TAPVR
Total Anomalous Pulmonary Venous Return 1
AQL
BL CF CI CL CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI
cui
C4551905
C4551904
C0036400
C4551903
DC
1
definition
An anomalous pulmonary venous return in which the right PULMONARY VEIN is not connected to the LEFT ATRIUM but to the INFERIOR VENA CAVA. Scimitar syndrome is named for the crescent- or Turkish sword-like shadow in the chest radiography and is often associated with hypoplasia of the right lung and right pulmonary artery, and dextroposition of the heart.
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