Preferred Name

vasculitis

Synonyms

systemic vasculitis

Definitions

Vasculitis represents a clinically heterogenous group of diseases of multifactorial etiology characterized by inflammation of either large-sized vessels (large-vessel vasculitis, e.g. Giant-cell arteritis and Takayasu arteritis), medium-sized vessels (medium-vessel vasculitis e.g. polyarteritis nodosa and Kawasaki disease), or small-sized vessels (small-vessel vasculitis, e.g. granulomatosis with polyangiitis, microscopic polyangiitis, immunoglobulin A vasculitis, and cutaneous leukocytoclastic angiitis). Vasculitis occurs at any age, may be acute or chronic, and manifests with general symptoms such as fever, weight loss and fatigue, as well as more specific clinical signs depending on the type of vessels and organs affected. The degree of severity is variable, ranging from life or sight threatening disease (e.g. BehC'et disease) to relatively minor skin disease.

ID

http://purl.obolibrary.org/obo/MONDO_0018882

has narrow synonym

systemic vasculitis

hasDbXref

SCTID:31996006

MESH:D014657

Orphanet:52759

GARD:0009565

MedDRA:10047115

UMLS:C0042384

Orphanet:280369

MedDRA:10036023

Wikipedia:Vasculitis

NCIT:C26912

EFO:0006803

DOID:865

imported from

http://purl.obolibrary.org/obo/mondo.owl

inSubset

http://purl.oboInOwllibrary.org/oboInOwl/mondo#rare

http://purl.oboInOwllibrary.org/oboInOwl/mondo#ordo_group_of_disorders

http://purl.oboInOwllibrary.org/oboInOwl/mondo#mondo_rare

http://purl.oboInOwllibrary.org/oboInOwl/mondo#disease_grouping

http://purl.oboInOwllibrary.org/oboInOwl/mondo#orphanet_rare

label

vasculitis

prefixIRI

MONDO:0018882

prefLabel

vasculitis

textual definition

Vasculitis represents a clinically heterogenous group of diseases of multifactorial etiology characterized by inflammation of either large-sized vessels (large-vessel vasculitis, e.g. Giant-cell arteritis and Takayasu arteritis), medium-sized vessels (medium-vessel vasculitis e.g. polyarteritis nodosa and Kawasaki disease), or small-sized vessels (small-vessel vasculitis, e.g. granulomatosis with polyangiitis, microscopic polyangiitis, immunoglobulin A vasculitis, and cutaneous leukocytoclastic angiitis). Vasculitis occurs at any age, may be acute or chronic, and manifests with general symptoms such as fever, weight loss and fatigue, as well as more specific clinical signs depending on the type of vessels and organs affected. The degree of severity is variable, ranging from life or sight threatening disease (e.g. BehC'et disease) to relatively minor skin disease.

subClassOf

http://purl.obolibrary.org/obo/MONDO_0005385

http://purl.obolibrary.org/obo/MONDO_0021166

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Delete Mapping To Ontology Source
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