Preferred Name

Optic Nerve Glioma

Synonyms

Optic Glioma|Glioblastoma Multiforme|Malignant Optic Nerve Astrocytoma

ID

http://bioontology.org/projects/ontologies/birnlex#birnlex_12621

abbrev

class_or_indiv

true

definition

Glial cell derived tumors arising from the optic nerve, usually presenting in childhood. Roughly 50% are associated with NEUROFIBROMATOSIS 1. Clinical manifestations include decreased visual acuity; EXOPHTHALMOS; NYSTAGMUS, PATHOLOGIC; STRABISMUS; pallor or swelling of the optic disc; and INTRACRANIAL HYPERTENSION. The tumor may extend into the optic chiasm and hypothalamus (MeSH).

external_id_urls

http://www.nlm.nih.gov/cgi/mesh/2008/MB_cgi?field=uid&term=D020339

external_ids

meshUID:D020339

label

Optic Nerve Glioma

mod_date

2007-10-05

preferred_label

Optic Nerve Glioma

prefixIRI

birnlex_12621

retired

false

synonyms

Optic Glioma|Glioblastoma Multiforme|Malignant Optic Nerve Astrocytoma

subClassOf

http://bioontology.org/projects/ontologies/birnlex#birnlex_12619

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