loading...| Preferred Name |
Alveolar Soft Part Sarcoma |
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| Synonyms |
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| Definitions |
A rare malignant neoplasm characterized by the presence of large epithelioid cells with abundant cytoplasm forming nests and pseudoalveolar structures. The groups of the epithelioid cells are separated by thin-walled sinusoidal spaces. It occurs most often in adolescents and young adults. In adults the most common sites of involvement are the extremities, and in infants and children, the head and neck. It usually presents as a slowly growing mass and it frequently metastasizes to other anatomic sites. The most common sites of metastasis are the lungs, bone, and brain. |
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| ID |
http://purl.obolibrary.org/obo/NCIT_C3750 |
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| ALT_DEFINITION |
A soft tissue tumor that is most common in older children and teenagers. It begins in the soft supporting tissue that connects and surrounds the organs and other tissues. Alveolar soft part sarcoma usually occurs in the legs, but can also occur in the arms, hands, head, or neck. It can cause the growth of new blood vessels that help the tumor grow and spread. |
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| code |
C3750 |
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| Contributing_Source |
Cellosaurus CPTAC CTEP CTRP GDC |
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| definition |
A rare malignant neoplasm characterized by the presence of large epithelioid cells with abundant cytoplasm forming nests and pseudoalveolar structures. The groups of the epithelioid cells are separated by thin-walled sinusoidal spaces. It occurs most often in adolescents and young adults. In adults the most common sites of involvement are the extremities, and in infants and children, the head and neck. It usually presents as a slowly growing mass and it frequently metastasizes to other anatomic sites. The most common sites of metastasis are the lungs, bone, and brain. |
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| Display_Name |
Alveolar Soft Part Sarcoma |
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| ICD-O-3_Code |
9581/3 |
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| in_subset |
http://purl.obolibrary.org/obo/NCIT_C168658 http://purl.obolibrary.org/obo/NCIT_C168656 http://purl.obolibrary.org/obo/NCIT_C168657 http://purl.obolibrary.org/obo/NCIT_C168655 http://purl.obolibrary.org/obo/NCIT_C102905 http://purl.obolibrary.org/obo/NCIT_C168662 http://purl.obolibrary.org/obo/NCIT_C168661 http://purl.obolibrary.org/obo/NCIT_C177537 http://purl.obolibrary.org/obo/ncit#oncotree_slim http://purl.obolibrary.org/obo/NCIT_C156952 http://purl.obolibrary.org/obo/NCIT_C156953 http://purl.obolibrary.org/obo/NCIT_C103117 http://purl.obolibrary.org/obo/NCIT_C116977 http://purl.obolibrary.org/obo/NCIT_C159414 http://purl.obolibrary.org/obo/NCIT_C165258 |
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| Is_Value_For_GDC_Property | ||
| label |
Alveolar Soft Part Sarcoma |
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| Legacy Concept Name |
Alveolar_Soft_Part_Sarcoma |
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| Maps_To |
Alveolar soft part sarcoma 9581/3 |
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| Neoplastic_Status |
Malignant |
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| Preferred_Name |
Alveolar Soft Part Sarcoma |
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| prefixIRI |
NCIT:C3750 |
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| prefLabel |
Alveolar Soft Part Sarcoma |
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| Semantic_Type |
Neoplastic Process |
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| UMLS_CUI |
C0206657 |
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| subClassOf |
http://purl.obolibrary.org/obo/NCIT_C9415 http://purl.obolibrary.org/obo/NCIT_C6588 |