Preferred Name |
Lymphangioleiomyomatosis |
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Synonyms |
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|
Definitions |
A multifocal neoplasm with perivascular epithelioid cell differentiation affecting almost exclusively females of child-bearing age. It is characterized by the presence of smooth muscle and epithelioid cells and by the proliferation of lymphatic vessels. Sites of involvement include the lungs, mediastinum, and the retroperitoneum. It usually presents with chylous pleural effusion or ascites. |
|
ID |
http://purl.obolibrary.org/obo/NCIT_C3725 |
|
code |
C3725 |
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Contributing_Source |
Cellosaurus CTRP GDC |
|
definition |
A multifocal neoplasm with perivascular epithelioid cell differentiation affecting almost exclusively females of child-bearing age. It is characterized by the presence of smooth muscle and epithelioid cells and by the proliferation of lymphatic vessels. Sites of involvement include the lungs, mediastinum, and the retroperitoneum. It usually presents with chylous pleural effusion or ascites. |
|
Display_Name |
Lymphangioleiomyomatosis |
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ICD-O-3_Code |
9174/1 |
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in_subset |
http://purl.obolibrary.org/obo/NCIT_C168658 http://purl.obolibrary.org/obo/NCIT_C168656 http://purl.obolibrary.org/obo/NCIT_C168657 http://purl.obolibrary.org/obo/NCIT_C168655 http://purl.obolibrary.org/obo/NCIT_C168662 http://purl.obolibrary.org/obo/NCIT_C168661 http://purl.obolibrary.org/obo/NCIT_C177537 http://purl.obolibrary.org/obo/NCIT_C116977 http://purl.obolibrary.org/obo/NCIT_C165258 |
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Is_Value_For_GDC_Property | ||
label |
Lymphangioleiomyomatosis |
|
Legacy Concept Name |
Lymphangiomyomatosis |
|
Maps_To |
Lymphangiomyomatosis Lymphangioleiomyomatosis 9174/1 |
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Neoplastic_Status |
Undetermined |
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Preferred_Name |
Lymphangioleiomyomatosis |
|
prefixIRI |
NCIT:C3725 |
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prefLabel |
Lymphangioleiomyomatosis |
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Semantic_Type |
Neoplastic Process |
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UMLS_CUI |
C0751674 |
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subClassOf |