Preferred Name |
Landau-Kleffner syndrome |
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Synonyms |
Acquired epileptic aphasia |
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Definitions |
Landau-Kleffner syndrome (LKS) is an age-related epileptic encephalopathy where developmental regression occurs mainly in the language domain and the electroencephalographic (EEG) abnormalities are mainly localized around the temporal-parietal regions. The term acquired epileptic aphasia describes the main features of this condition. |
|
ID |
http://www.orpha.net/ORDO/Orphanet_98818 |
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alternative_term |
Acquired epileptic aphasia LKS |
|
definition |
Landau-Kleffner syndrome (LKS) is an age-related epileptic encephalopathy where developmental regression occurs mainly in the language domain and the electroencephalographic (EEG) abnormalities are mainly localized around the temporal-parietal regions. The term acquired epileptic aphasia describes the main features of this condition. |
|
definition_citation |
Orphanet |
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expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=98818 |
|
has_age_of_onset |
Childhood |
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has_inheritance |
Autosomal dominant |
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hasDbXref |
MedDRA:10052075 MeSH:D018887 UMLS:C0282512 ICD-10:F80.3 OMIM:245570 ICD-11:8A62.2 |
|
label |
Landau-Kleffner syndrome |
|
notation |
ORPHA:98818 |
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part_of | ||
prefixIRI |
ORDO:Orphanet_98818 |
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prefLabel |
Landau-Kleffner syndrome |
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present_in |
Japan AND has_point_prevalence_average_value : 0.4 AND has_point_prevalence_range : 1-9 / 1 000 000 |
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treeView | ||
subClassOf |