Preferred Name | Sporotrichosis | |
Synonyms |
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Definitions |
Sporotrichosis is an infection caused by the dimorphic fungus <i>Sporothrix schenckii</i>, generally occurring by traumatic inoculation of fungus from contaminated soil, plants, and organic matter, that has a highly variable disease spectrum but that usually presents as a subcutaneous mycosis with a single sporotrichotic chancre that may ulcerate and can then progress to lymphocutaneous (most common form; sporotrichotic chancre at inoculation site and a string of similar nodules along the proximal lymphatics), fixed cutaneous (localized asymptomatic, erythematous, papules at the inoculation site), or multifocal or disseminated cutaneous (rare form, with 3 or more lesions involving 2 different anatomical sites) forms. Pulmonary sporotrichosis occurs following inhalation of fungus and manifests as chronic pneumonitis while extracutaneous or systemic sporotrichosis (with osteoarticular, pulmonary, and central nervous system/meningeal disease) has also been reported, usually occurring in the setting of immunosuppression. |
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ID |
http://www.orpha.net/ORDO/Orphanet_826 |
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definition |
Sporotrichosis is an infection caused by the dimorphic fungus Sporothrix schenckii, generally occurring by traumatic inoculation of fungus from contaminated soil, plants, and organic matter, that has a highly variable disease spectrum but that usually presents as a subcutaneous mycosis with a single sporotrichotic chancre that may ulcerate and can then progress to lymphocutaneous (most common form; sporotrichotic chancre at inoculation site and a string of similar nodules along the proximal lymphatics), fixed cutaneous (localized asymptomatic, erythematous, papules at the inoculation site), or multifocal or disseminated cutaneous (rare form, with 3 or more lesions involving 2 different anatomical sites) forms. Pulmonary sporotrichosis occurs following inhalation of fungus and manifests as chronic pneumonitis while extracutaneous or systemic sporotrichosis (with osteoarticular, pulmonary, and central nervous system/meningeal disease) has also been reported, usually occurring in the setting of immunosuppression. |
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definition_citation |
Orphanet |
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expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=826 |
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has_age_of_onset |
All ages |
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has_inheritance |
Not applicable |
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hasDbXref |
ICD-10:B42.7 ICD-11:1F2J.3 ICD-11:1F2J.2 ICD-11:1F2J.0 ICD-11:1F2J.1 ICD-11:1F2J.Y ICD-10:B42.1 ICD-10:B42.9 ICD-10:B42.8 UMLS:C0038034 MeSH:D013174 ICD-10:B42.0 MedDRA:10041736 ICD-11:1F2J |
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label |
Sporotrichosis |
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notation |
ORPHA:826 |
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part_of | ||
prefixIRI |
ORDO:Orphanet_826 |
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prefLabel |
Sporotrichosis |
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present_in |
Peru AND has_annual_incidence_average_value : 54.0 AND has_annual_incidence_range : 1-5 / 10 000 Mexico AND has_point_prevalence_average_value : 2500.0 AND has_point_prevalence_range : >1 / 1000 Worldwide AND has_point_prevalence_range : Unknown |
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treeView | ||
subClassOf |