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Orphanet Rare Disease Ontology
Last uploaded:
July 3, 2024
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| Preferred Name | Bullous pemphigoid | |
| Synonyms |
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| Definitions |
A rare autoimmune bullous skin disease characterized by acquired, subepidermal tense bullae occurring on normal of inflamed skin and that is typically widespread (occurring in the flexor regions of the proximal arms and legs, in the armpits, groin and the abdomen) and often associated with pruritus. The evolution is typically chronic with spontaneous exacerbations and remission. |
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| ID |
http://www.orpha.net/ORDO/Orphanet_703 |
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| definition |
A rare autoimmune bullous skin disease characterized by acquired, subepidermal tense bullae occurring on normal of inflamed skin and that is typically widespread (occurring in the flexor regions of the proximal arms and legs, in the armpits, groin and the abdomen) and often associated with pruritus. The evolution is typically chronic with spontaneous exacerbations and remission.
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| definition_citation |
Orphanet
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| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=703 |
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| has_age_of_onset |
All ages
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| has_inheritance |
Not applicable
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| hasDbXref |
MedDRA:10006567 ICD-10:L12.0 UMLS:C0030805 ICD-11:EB41.0 MeSH:D010391
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| label |
Bullous pemphigoid
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| notation |
ORPHA:703
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| part_of | ||
| prefixIRI |
ORDO:Orphanet_703
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| prefLabel |
Bullous pemphigoid
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| present_in |
Germany AND has_annual_incidence_average_value : 1.34 AND has_annual_incidence_range : 1-9 / 100 000 France AND has_annual_incidence_average_value : 2.17 AND has_annual_incidence_range : 1-9 / 100 000 Germany AND has_point_prevalence_average_value : 25.93 AND has_point_prevalence_range : 1-5 / 10 000 Switzerland AND has_annual_incidence_average_value : 1.21 AND has_annual_incidence_range : 1-9 / 100 000 United Kingdom AND has_annual_incidence_average_value : 4.3 AND has_annual_incidence_range : 1-9 / 100 000 Europe AND has_point_prevalence_average_value : 25.0 AND has_point_prevalence_range : 1-5 / 10 000
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