Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Pyoderma gangrenosum

Synonyms
Definitions

Pyoderma gangrenosum (PG) is a primarily sterile inflammatory neutrophilic dermatosis characterized by recurrent cutaneous ulcerations with a mucopurulent or hemorrhagic exudate.

ID

http://www.orpha.net/ORDO/Orphanet_48104

definition

Pyoderma gangrenosum (PG) is a primarily sterile inflammatory neutrophilic dermatosis characterized by recurrent cutaneous ulcerations with a mucopurulent or hemorrhagic exudate.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=48104

has_age_of_onset

Adolescent

Adult

Childhood

Elderly

has_inheritance

Unknown

hasDbXref

MeSH:D017511

UMLS:C0085652

MedDRA:10037635

ICD-11:EB21

ICD-10:L88

label

Pyoderma gangrenosum

notation

ORPHA:48104

part_of

http://www.orpha.net/ORDO/Orphanet_290842

http://www.orpha.net/ORDO/Orphanet_324927

prefixIRI

ORDO:Orphanet_48104

prefLabel

Pyoderma gangrenosum

present_in

Italy AND has_annual_incidence_average_value : 0.517 AND has_annual_incidence_range : 1-9 / 1 000 000

United States AND has_annual_incidence_average_value : 1.0 AND has_annual_incidence_range : 1-9 / 100 000

Spain AND has_annual_incidence_average_value : 0.33 AND has_annual_incidence_range : 1-9 / 1 000 000

United Kingdom AND has_annual_incidence_average_value : 0.91 AND has_annual_incidence_range : 1-9 / 1 000 000

Worldwide AND has_annual_incidence_average_value : 0.74 AND has_annual_incidence_range : 1-9 / 1 000 000

Worldwide AND has_point_prevalence_range : Unknown

treeView

http://www.orpha.net/ORDO/Orphanet_290842

http://www.orpha.net/ORDO/Orphanet_324927

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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Delete Mapping To Ontology Source
http://www.ebi.ac.uk/efo/EFO_0006835 EFO LOOM
http://purl.obolibrary.org/obo/MONDO_0018824 MONDO LOOM
http://purl.obolibrary.org/obo/DOID_8553 DOID LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_8553 NATPRO LOOM
http://purl.bioontology.org/ontology/ICD10CM/L88 NLMVS LOOM
http://purl.bioontology.org/ontology/ICD10CM/L88 ICD10CM LOOM
http://purl.bioontology.org/ontology/ICPC2P/S76008 ICPC2P LOOM
http://purl.bioontology.org/ontology/MEDDRA/10037635 MEDDRA LOOM
http://purl.bioontology.org/ontology/AIR/PYGAN AI-RHEUM LOOM
http://www.limics.org/hrdo/rdfns#pat_id_10613 HRDO LOOM
http://purl.obolibrary.org/obo/MONDO_0018824 DOVES LOOM
http://www.gamuts.net/entity#pyoderma_gangrenosum GAMUTS LOOM
http://purl.bioontology.org/ontology/MESH/D017511 MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C17.800.862.675 RH-MESH LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0085652 OCHV LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D017511 RH-MESH LOOM
http://purl.bioontology.org/ontology/RCD/M0702 RCD LOOM
http://purl.obolibrary.org/obo/DERMO_0000331 DERMO LOOM
http://purl.bioontology.org/ontology/RCTV2/M070200 RCTV2 LOOM
http://purl.bioontology.org/ontology/ICD10/L88 ICD10 LOOM
http://www.semanticweb.org/ontologies/2012/5/Ontology1338526551855.owl#Pyoderma_gangrenosum RPO LOOM
http://id.nlm.nih.gov/mesh/D017511 MDM LOOM
http://purl.obolibrary.org/obo/OMIT_0017861 OMIT LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/74578003 SNOMEDCT LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU038674 OMIM LOOM
http://www.phoc.org.cn/pmo/class/PMO_00039314 PMAPP-PMO LOOM
http://purl.bioontology.org/ontology/SNMI/D0-01603 SNMI LOOM
http://purl.bioontology.org/ontology/WHO/1339 WHO-ART LOOM
http://purl.obolibrary.org/obo/DOID_8553 DTO LOOM
http://purl.obolibrary.org/obo/DOID_8553 BAO LOOM
http://purl.obolibrary.org/obo/DOID_8553 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_8553 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_8553 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_8553 FNS-H LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C17.800.695.675 RH-MESH LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#15710 OCHV LOOM
http://purl.obolibrary.org/obo/HP_0025452 HP LOOM
http://purl.obolibrary.org/obo/HP_0025452 UPHENO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C17.800.893.675 RH-MESH LOOM
http://www.owl-ontologies.com/unnamed.owl#RID15583 DERMLEX LOOM
http://purl.bioontology.org/ontology/ICD9CM/686.01 ICD9CM LOOM
http://purl.bioontology.org/ontology/ICD9CM/686.01 NLMVS LOOM
http://www.gamuts.net/entity#pyoderma_gangrenosum GAMUTS REST