Orphanet Rare Disease Ontology

Last uploaded: July 3, 2024
Preferred Name

Anaplastic oligodendroglioma
Synonyms
Definitions

A rare glial tumor characterized by a grade III oligodendroglial tumour with focal or diffuse anaplastic features. It typically occurs in the supratentorial white matter. Histologically, the cells are enlarged and epithelioid with pleomorphic and increased size nuclei, a vesicular chromatin pattern and prominent nucleoli. Most patients present with seizures.

ID

http://www.orpha.net/ORDO/Orphanet_251630

definition

A rare glial tumor characterized by a grade III oligodendroglial tumour with focal or diffuse anaplastic features. It typically occurs in the supratentorial white matter. Histologically, the cells are enlarged and epithelioid with pleomorphic and increased size nuclei, a vesicular chromatin pattern and prominent nucleoli. Most patients present with seizures.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=251630

has_age_of_onset

Adult

has_inheritance

Not applicable

hasDbXref

ICD-11:XH8844

ICD-11:2A00.0Y

OMIM:137800

ICD-11:XH9QF3

ICD-10:C71.9

UMLS:C0334590

MedDRA:10026659

label

Anaplastic oligodendroglioma

notation

ORPHA:251630

part_of

http://www.orpha.net/ORDO/Orphanet_46484

prefixIRI

ORDO:Orphanet_251630

prefLabel

Anaplastic oligodendroglioma

present_in

Europe AND has_annual_incidence_average_value : 0.09 AND has_annual_incidence_range : <1 / 1 000 000

United States AND has_annual_incidence_average_value : 0.11 AND has_annual_incidence_range : 1-9 / 1 000 000

treeView

http://www.orpha.net/ORDO/Orphanet_46484

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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