loading...| Preferred Name |
Aggressive Systemic Mastocytosis |
|
| Synonyms |
Aggressive systemic mastocytosis Aggressive Systemic Mastocytosis Advanced Systemic Mastocytosis ASM |
|
| Definitions |
An aggressive and progressive mast cell neoplasm characterized by systemic infiltration of internal organs by aggregates of neoplastic mast cells. There is no evidence of mast cell leukemia or clonal hematologic malignancy. Clinical symptoms include hepatomegaly, splenomegaly, portal hypertension, malabsorption syndrome, and pathologic fractures. |
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| ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C9285 |
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| code |
C9285 |
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| Concept_In_Subset |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C157711 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193175 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C116977 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193248 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C126659 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C118168 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193231 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193006 |
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| Contributing_Source |
CTRP GDC mCode |
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| DEFINITION |
An aggressive and progressive mast cell neoplasm characterized by systemic infiltration of internal organs by aggregates of neoplastic mast cells. There is no evidence of mast cell leukemia or clonal hematologic malignancy. Clinical symptoms include hepatomegaly, splenomegaly, portal hypertension, malabsorption syndrome, and pathologic fractures. |
|
| Display_Name |
Aggressive Systemic Mastocytosis |
|
| FULL_SYN |
Aggressive systemic mastocytosis Aggressive Systemic Mastocytosis Advanced Systemic Mastocytosis ASM |
|
| ICD-O-3_Code |
9741/3 |
|
| Is_Value_For_GDC_Property | ||
| label |
Aggressive Systemic Mastocytosis |
|
| Legacy Concept Name |
Aggressive_Systemic_Mastocytosis |
|
| Maps_To |
Aggressive systemic mastocytosis 9741/3 |
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| Neoplastic_Status |
Malignant |
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| Preferred_Name |
Aggressive Systemic Mastocytosis |
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| prefixIRI |
Thesaurus:C9285 |
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| Semantic_Type |
Neoplastic Process |
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| UMLS_CUI |
C1112486 |
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| subClassOf |