National Cancer Institute Thesaurus

Last uploaded: February 23, 2024
Preferred Name

Anaplastic Ependymoma

Synonyms

WHO Grade III Ependymal Neoplasm

Undifferentiated Ependymal Tumor

Undifferentiated Ependymal Neoplasm

Anaplastic Ependymal Neoplasm

Anaplastic Ependymal Tumor

WHO Grade 3 Ependymal Neoplasm

WHO Grade 3 Ependymal Tumor

Malignant Ependymoma

Anaplastic Ependymoma

Ependymoma with Anaplasia

Undifferentiated Ependymoma

Ependymoma, anaplastic

WHO Grade III Ependymal Tumor

Definitions

A WHO grade 3 malignant glioma of ependymal origin with accelerated growth and an unfavorable clinical outcome, particularly in children. It is characterized by high mitotic activity, often accompanied by microvascular proliferation and pseudo-palisading necrosis. (Adapted from WHO)

ID

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C4049

code

C4049

Concept_In_Subset

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C157711

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C156952

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168661

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168656

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168662

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C156966

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168658

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C126659

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168655

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C158520

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168657

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C177537

Contributing_Source

CPTAC

GDC

DEFINITION

A WHO grade 3 malignant glioma of ependymal origin with accelerated growth and an unfavorable clinical outcome, particularly in children. It is characterized by high mitotic activity, often accompanied by microvascular proliferation and pseudo-palisading necrosis. (Adapted from WHO)

FULL_SYN

WHO Grade III Ependymal Neoplasm

Undifferentiated Ependymal Tumor

Undifferentiated Ependymal Neoplasm

Anaplastic Ependymal Neoplasm

Anaplastic Ependymal Tumor

WHO Grade 3 Ependymal Neoplasm

WHO Grade 3 Ependymal Tumor

Malignant Ependymoma

Anaplastic Ependymoma

Ependymoma with Anaplasia

Undifferentiated Ependymoma

Ependymoma, anaplastic

WHO Grade III Ependymal Tumor

ICD-O-3_Code

9392/3

Is_Value_For_GDC_Property

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C177621

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C176985

label

Anaplastic Ependymoma

Legacy Concept Name

Anaplastic_Ependymoma

Maps_To

Ependymoma, anaplastic

9392/3

Neoplastic_Status

Malignant

Preferred_Name

Anaplastic Ependymoma

prefixIRI

Thesaurus:C4049

Semantic_Type

Neoplastic Process

UMLS_CUI

C0280788

subClassOf

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C6770

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C36025

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C127816

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