Mondo Disease Ontology

Last uploaded: May 9, 2024
Preferred Name

capillary leak syndrome

Synonyms

CLS

capillary leak syndrome

capillary hyperpermeability syndrome

acute vascular leak syndrome

systemic capillary leak syndrome

idiopathic capillary leak syndrome

Clarkson disease

AVLS

SCLS

capillary leak syndrome with monoclonal gammopathy

periodic systemic capillary leak syndrome

Definitions

A syndrome characterized by leakage of intravascular fluids into the extravascular space. This syndrome is observed in patients who demonstrate a state of generalized leaky capillaries following shock syndromes, low-flow states, ischemia-reperfusion injuries, toxemias, medications, or poisoning. It can lead to generalized edema and multiple organ failure.

ID

http://purl.obolibrary.org/obo/MONDO_0001956

closeMatch

http://identifiers.org/meddra/10007196

database_cross_reference

Orphanet:188

EFO:1001284

MESH:D019559

GARD:1084

ICD9:448.9

DOID:14400

UMLS:C0343084

NCIT:C62578

SCTID:87730004

MedDRA:10007196

definition

A syndrome characterized by leakage of intravascular fluids into the extravascular space. This syndrome is observed in patients who demonstrate a state of generalized leaky capillaries following shock syndromes, low-flow states, ischemia-reperfusion injuries, toxemias, medications, or poisoning. It can lead to generalized edema and multiple organ failure.

exactMatch

http://identifiers.org/snomedct/87730004

http://purl.obolibrary.org/obo/DOID_14400

http://identifiers.org/mesh/D019559

http://linkedlifedata.com/resource/umls/id/C0343084

http://purl.obolibrary.org/obo/NCIT_C62578

http://purl.obolibrary.org/obo/Orphanet_188

has_exact_synonym

CLS

capillary leak syndrome

capillary hyperpermeability syndrome

acute vascular leak syndrome

systemic capillary leak syndrome

idiopathic capillary leak syndrome

Clarkson disease

AVLS

SCLS

has_related_synonym

capillary leak syndrome with monoclonal gammopathy

periodic systemic capillary leak syndrome

id

MONDO:0001956

in_subset

http://purl.obolibrary.org/obo/mondo#ordo_disease

http://purl.obolibrary.org/obo/mondo#rare

http://purl.obolibrary.org/obo/mondo#orphanet_rare

http://purl.obolibrary.org/obo/mondo#otar

http://purl.obolibrary.org/obo/mondo#gard_rare

label

capillary leak syndrome

notation

MONDO:0001956

prefLabel

capillary leak syndrome

treeView

http://purl.obolibrary.org/obo/MONDO_0001574

http://purl.obolibrary.org/obo/MONDO_0002254

subClassOf

http://purl.obolibrary.org/obo/MONDO_0001574

http://purl.obolibrary.org/obo/MONDO_0002254

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Delete Mapping To Ontology Source
http://purl.obolibrary.org/obo/MONDO_0001956 DOVES SAME_URI
http://www.ebi.ac.uk/efo/EFO_1001284 EFO LOOM
http://purl.obolibrary.org/obo/DOID_14400 CVDO LOOM
http://purl.obolibrary.org/obo/DOID_14400 DOID LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#30831 OCHV LOOM
http://purl.jp/bio/4/id/200906079081525562 IOBC LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/ctcae5.owl#C143349 CTCAE LOOM
http://purl.bioontology.org/ontology/SNMI/D3-85128 SNMI LOOM
http://www.phoc.org.cn/pmo/class/PMO_00036312 PMAPP-PMO LOOM
http://purl.obolibrary.org/obo/DOID_14400 BAO LOOM
http://purl.obolibrary.org/obo/DOID_14400 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_14400 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_14400 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_14400 FNS-H LOOM
http://purl.obolibrary.org/obo/MONDO_0001956 DOVES LOOM
http://purl.obolibrary.org/obo/CCTO_001086 CCTOO LOOM
http://purl.bioontology.org/ontology/MESH/D019559 MESH LOOM
http://purl.bioontology.org/ontology/MEDDRA/10007196 MEDDRA LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C62578 NCIT LOOM
http://purl.obolibrary.org/obo/OMIT_0019584 OMIT LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/87730004 SNOMEDCT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D019559 RH-MESH LOOM
http://www.owl-ontologies.com/unnamed.owl#RID18952 DERMLEX LOOM
http://purl.obolibrary.org/obo/NCIT_C62578 BERO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0343084 OCHV LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C14.907.218 RH-MESH LOOM
http://purl.bioontology.org/ontology/RCD/X50B1 RCD LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_14400 NATPRO LOOM