Preferred Name |
Moyamoya Disease |
|
Synonyms |
Disease, Primary Moyamoya |
|
Definitions |
A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults. |
|
ID |
http://purl.bioontology.org/ontology/MESH/D009072 |
|
altLabel |
Disease, Primary Moyamoya Moyamoya Disease, Primary Moya Moya Disease Progressive Intracranial Occlusive Arteropathy (Moyamoya) Primary Moyamoya Diseases Moyamoya Disease, Secondary Moya-Moya Disease Secondary Moyamoya Disease Classic Moyamoya Disease Disease, Classic Moyamoya Cerebrovascular Moyamoya Disease Moyamoya Syndrome Primary Moyamoya Disease Moyamoya Disease, Classic Disease, Moya-Moya Moyamoya Diseases, Primary |
|
AQL |
BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI |
|
cui |
C0026654 C0751322 C0751323 |
|
DC |
1 |
|
definition |
A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults. |
|
DX |
19910101 |
|
HN |
1991(1978) |
|
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000178 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000469 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000209 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000652 |
|
Machine permutation |
1991; see ARTERIAL OCCLUSIVE DISEASES 1978-1990 |
|
Mapped from |
http://purl.bioontology.org/ontology/MESH/C536993 |
|
MDA |
19770427 |
|
MMR |
20120703 |
|
MN |
C14.907.253.123.620 C14.907.137.615 C10.228.140.300.510.200.737 C14.907.253.560.200.737 C10.228.140.300.200.600 |
|
notation |
D009072 |
|
prefLabel |
Moyamoya Disease |
|
TERMUI |
T369517 T369520 T369516 T027090 T369521 T369519 T369518 T027091 |
|
TH |
OMIM (2013) NLM (2000) NLM (1999) NLM (1978) ORD (2010) |
|
tui |
T047 |
|
subClassOf |
http://purl.bioontology.org/ontology/MESH/D002340 |