Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Moyamoya Disease

Synonyms

Disease, Primary Moyamoya

Definitions

A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults.

ID

http://purl.bioontology.org/ontology/MESH/D009072

altLabel

Disease, Primary Moyamoya

Moyamoya Disease, Primary

Moya Moya Disease

Progressive Intracranial Occlusive Arteropathy (Moyamoya)

Primary Moyamoya Diseases

Moyamoya Disease, Secondary

Moya-Moya Disease

Secondary Moyamoya Disease

Classic Moyamoya Disease

Disease, Classic Moyamoya

Cerebrovascular Moyamoya Disease

Moyamoya Syndrome

Primary Moyamoya Disease

Moyamoya Disease, Classic

Disease, Moya-Moya

Moyamoya Diseases, Primary

AQL

BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI

cui

C0026654

C0751322

C0751323

DC

1

definition

A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults.

DX

19910101

HN

1991(1978)

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Machine permutation

1991; see ARTERIAL OCCLUSIVE DISEASES 1978-1990

Mapped from

http://purl.bioontology.org/ontology/MESH/C536993

http://purl.bioontology.org/ontology/MESH/C536992

http://purl.bioontology.org/ontology/MESH/C536991

MDA

19770427

MMR

20120703

MN

C14.907.253.123.620

C14.907.137.615

C10.228.140.300.510.200.737

C14.907.253.560.200.737

C10.228.140.300.200.600

notation

D009072

prefLabel

Moyamoya Disease

TERMUI

T369517

T369520

T369516

T027090

T369521

T369519

T369518

T027091

TH

OMIM (2013)

NLM (2000)

NLM (1999)

NLM (1978)

ORD (2010)

tui

T047

subClassOf

http://purl.bioontology.org/ontology/MESH/D002340

http://purl.bioontology.org/ontology/MESH/D001157

http://purl.bioontology.org/ontology/MESH/D002539

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http://purl.bioontology.org/ontology/MSHFRE/D009072 MSHFRE CUI
http://purl.bioontology.org/ontology/SNOMEDCT/1208841001 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MDRGER/10028047 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10067590 MDRGER CUI
http://purl.bioontology.org/ontology/SCTSPA/89142007 SCTSPA CUI
http://purl.bioontology.org/ontology/OMIM/MTHU023633 OMIM CUI
http://purl.bioontology.org/ontology/ICD10CM/I67.5 ICD10CM CUI
http://purl.bioontology.org/ontology/ICD9CM/437.5 ICD9CM CUI
http://purl.bioontology.org/ontology/MEDDRA/10028047 MEDDRA CUI
http://purl.bioontology.org/ontology/RCD/G675. RCD CUI
http://purl.bioontology.org/ontology/MEDDRA/10067590 MEDDRA CUI
http://purl.bioontology.org/ontology/NDFRT/N0000002040 NDFRT CUI
http://purl.bioontology.org/ontology/MDRFRE/10067590 MDRFRE CUI
http://purl.bioontology.org/ontology/OMIM/MTHU037610 OMIM CUI
http://purl.bioontology.org/ontology/ICD10/I67.5 ICD10 CUI
http://purl.bioontology.org/ontology/SNMI/D3-89630 SNMI CUI
http://purl.bioontology.org/ontology/SCTSPA/69116000 SCTSPA CUI
http://purl.bioontology.org/ontology/OMIM/MTHU041200 OMIM CUI
http://purl.bioontology.org/ontology/MSHFRE/D009072 MSHFRE CUI
http://purl.bioontology.org/ontology/SNOMEDCT/69116000 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MDRFRE/10028047 MDRFRE CUI
http://purl.bioontology.org/ontology/SNOMEDCT/89142007 SNOMEDCT CUI
http://purl.bioontology.org/ontology/SNMI/D3-89402 SNMI CUI
http://purl.bioontology.org/ontology/SCTSPA/1208841001 SCTSPA CUI
http://purl.bioontology.org/ontology/MSHFRE/D009072 MSHFRE CUI
http://purl.obolibrary.org/obo/MONDO_0016820 MONDO LOOM
http://purl.obolibrary.org/obo/MONDO_0016820 EFO LOOM
http://purl.obolibrary.org/obo/DOID_13099 DOID LOOM
http://nanbyodata.jp/ontology/NANDO_2200850 NANDO LOOM
http://nanbyodata.jp/ontology/NANDO_2100228 NANDO LOOM
http://nanbyodata.jp/ontology/NANDO_1200183 NANDO LOOM
http://purl.obolibrary.org/obo/DOID_13099 DTO LOOM
http://purl.obolibrary.org/obo/DOID_13099 BAO LOOM
http://purl.obolibrary.org/obo/DOID_13099 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_13099 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_13099 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_13099 FNS-H LOOM
http://purl.jp/bio/4/id/200906089025721931 IOBC LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#8296 OCHV LOOM
http://www.semanticweb.org/ontologies/2012/5/Ontology1338526551855.owl#Moyamoya_Disease RPO LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_13099 NATPRO LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU023633 OMIM LOOM
http://purl.obolibrary.org/obo/OMIT_0010115 OMIT LOOM
http://purl.bioontology.org/ontology/ICD10CM/I67.5 ICD10CM LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.228.140.300.510.200.737 RH-MESH LOOM
http://purl.bioontology.org/ontology/ICD9CM/437.5 ICD9CM LOOM
http://purl.bioontology.org/ontology/MEDDRA/10028047 MEDDRA LOOM
http://purl.bioontology.org/ontology/RCD/G675. RCD LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C84895 NCIT LOOM
http://radlex.org/RID/RID38605 RADLEX LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C14.907.137.615 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D009072 RH-MESH LOOM
http://purl.bioontology.org/ontology/RCTV2/G675.00 RCTV2 LOOM
http://purl.bioontology.org/ontology/ICD10/I67.5 ICD10 LOOM
http://purl.bioontology.org/ontology/SNMI/D3-89630 SNMI LOOM
http://www.orpha.net/ORDO/Orphanet_2573 ORDO LOOM
http://purl.obolibrary.org/obo/MONDO_0016820 DOVES LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/69116000 SNOMEDCT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C14.907.253.560.200.737 RH-MESH LOOM
http://www.limics.org/hrdo/rdfns#pat_id_2373 HRDO LOOM
http://purl.obolibrary.org/obo/NCIT_C84895 BERO LOOM
http://www.co-ode.org/ontologies/galen#MoyamoyaDisease GALEN LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C14.907.253.123.620 RH-MESH LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Moyamoya_Disease CSEO LOOM
http://purl.obolibrary.org/obo/SCDO_0006833 SCDO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.228.140.300.200.600 RH-MESH LOOM
http://www.phoc.org.cn/pmo/class/PMO_00036330 PMAPP-PMO LOOM
http://www.semanticweb.org/ontologies/STO.owl#OWLClass_901b7fda_765b_41eb_83ba_c61dab4de81d STO-DRAFT LOOM
http://www.semanticweb.org/ontologies/STO.owl#OWLClass_901b7fda_765b_41eb_83ba_c61dab4de81d CVAO LOOM
http://www.ustb.edu.cn/thesauri/tocr/v1/data#C571342296272859179 ACVD_ONTOLOGY LOOM