Preferred Name |
thrombotic thrombocytopenic purpura |
|
Synonyms |
Moschcowitz disease TTP Moschowitz disease Moschcowitz's syndrome |
|
Definitions |
Thrombotic thrombocytopenic purpura (TTP) is an aggressive and life-threatening form of thrombotic microangiopathy (TMA) characterized by profound peripheral thrombocytopenia, microangiopathic hemolytic anemia (MAHA) and organ failure of variable severity and is comprised of congenital TTP and acquired TTP. |
|
ID |
http://purl.obolibrary.org/obo/MONDO_0018896 |
|
closeMatch |
http://identifiers.org/snomedct/360402008 http://identifiers.org/snomedct/195359000 |
|
database_cross_reference |
NCIT:C78797 Orphanet:54057 SCTID:78129009 COHD:4301602 UMLS:C0034155 MedDRA:10043648 MESH:D011697 DOID:10772 ICD10:M31.1 |
|
exactMatch |
http://purl.obolibrary.org/obo/NCIT_C78797 http://www.orpha.net/ORDO/Orphanet_54057 http://linkedlifedata.com/resource/umls/id/C0034155 http://identifiers.org/mesh/D011697 http://purl.obolibrary.org/obo/DOID_10772 |
|
has exact synonym |
Moschcowitz disease TTP Moschowitz disease Moschcowitz's syndrome |
|
id |
MONDO:0018896 |
|
imported from | ||
in_subset | ||
label |
thrombotic thrombocytopenic purpura |
|
notation |
MONDO:0018896 |
|
prefLabel |
thrombotic thrombocytopenic purpura |
|
textual definition |
Thrombotic thrombocytopenic purpura (TTP) is an aggressive and life-threatening form of thrombotic microangiopathy (TMA) characterized by profound peripheral thrombocytopenia, microangiopathic hemolytic anemia (MAHA) and organ failure of variable severity and is comprised of congenital TTP and acquired TTP. |
|
subClassOf |
http://purl.obolibrary.org/obo/MONDO_0016635 |