Preferred Name

Systemic mastocytosis

Synonyms

Mast cell disease

Mastócitos, doença de

Malattia dei mastociti

Doença de mastócitos

ID

http://www.limics.org/hrdo/rdfns#pat_id_887

ageOfDeath

Cualquier edad

Alle Alter

Qualquer idade

Tout âge

Any age

Qualsiasi età

Any age

ageOfOnset

Variable

Variabile

Variabel

Variable

Variable

Variável

Variable

altLabel

Mast cell disease

Doença de mastócitos

Malattia dei mastociti

Mastócitos, doença de

id_MedDRA

10042949

id_Medline

http://www.ncbi.nlm.nih.gov/sites/entrez?Db=pubmed&Cmd=Search&Term=systemic+mastocytosis%5Bti%5D+OR+mast+cell+disease%5Bti%5D+OR+Mastocytosis+Systemic%5Btw%5D+OR+%22mastocytosis%2C+systemic%22%5BMeSH+Terms%5D

id_MeSH

D034721

id_OMS

C96.2

id_Orpha

2467

id_SNOMEDCT

397016004

id_UMLS

C0221013

inheritance

Esporádico

Sporadic

Sporadisch

Sporadique

Sporadica

Sporadic

Esporádica

patType

group of phenomes

prefixIRI

hrdo:pat_id_887

prefLabel

Mastocitosi sistemica

Mastocitosis sistémica

Mastozytose, systemische

Mastocytose systémique

Systemic mastocytosis

Mastocitose sistémica

prevalence

1-9 / 100 000

1-9 / 100 000

1-9 / 100 000

1-9 / 100 000

1-9 / 100 000

1-9 / 100 000

1-9 / 100 000

subClassOf

http://www.limics.org/hrdo/rdfns#pat_id_13309

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