Preferred Name |
Primary biliary cirrhosis |
|
Synonyms |
Syndrome de Hanot Hanot-Zirrhose Sindrome di Hanot Hanot, síndrome de Hanot syndrome |
|
ID |
http://www.limics.org/hrdo/rdfns#pat_id_874 |
|
ageOfOnset |
Erwachsenenalter Adulte La edad adulta Età adulta Adulthood Adulthood Idade adulta |
|
altLabel |
Syndrome de Hanot Hanot-Zirrhose Sindrome di Hanot Hanot, síndrome de Hanot syndrome Síndrome de Hanot Síndrome de Hanot |
|
id_MedDRA |
10004661 10019137 |
|
id_Medline | ||
id_MIM |
109720 613007 613008 614220 614221 |
|
id_OMS |
K74.3 |
|
id_Orpha |
186 |
|
id_SNOMEDCT |
31712002 |
|
id_UMLS |
C0008312 C0859942 |
|
inheritance |
Multigénico/multifactorial Multigenica/multifattoriale Multigenic/multifactorial Polygénique/polyfactoriel Multigénica/multifactorial Multigenic/multifactorial Polygenetisch/Multifaktoriell |
|
patType |
disease |
|
prefixIRI |
hrdo:pat_id_874 |
|
prefLabel |
Cirrose biliar primária Primary biliary cirrhosis Cirrhose biliaire primitive Zirrhose, biliäre primäre Cirrosis biliar primaria Cirrosi biliare primitiva |
|
prevalence |
1-5 / 10 000 1-5 / 10 000 1-5 / 10 000 1-5 / 10 000 1-5 / 10 000 1-5 / 10 000 1-5 / 10 000 |
|
subClassOf |