Preferred Name |
Aggressive systemic mastocytosis |
|
Synonyms |
|
|
ID |
http://www.limics.org/hrdo/rdfns#pat_id_13867 |
|
ageOfOnset |
Erwachsenenalter Adulte La edad adulta Età adulta Adulthood Adulthood Idade adulta |
|
id_MedDRA |
10056453 |
|
id_Medline |
neant |
|
id_OMS |
C96.2 |
|
id_Orpha |
98850 |
|
id_SNOMEDCT |
397008008 397358005 |
|
id_UMLS |
C1112486 |
|
inheritance |
Esporádico Sporadic Sporadisch Sporadique Sporadica Sporadic Esporádica |
|
patType |
disease |
|
prefixIRI |
hrdo:pat_id_13867 |
|
prefLabel |
Mastocitosis sistémica agresiva Mastocytose systémique agressive Aggressive systemic mastocytosis Mastocitosi sistemica aggressiva Mastozytose, systemische, agressive Form Mastocitose sistémica agressiva |
|
prevalence |
1-9 / 1 000 000 1-9 / 1 000 000 1-9 / 1 000 000 1-9 / 1 000 000 1-9 / 1 000 000 1-9 / 1 000 000 1-9 / 1 000 000 |
|
subClassOf |
Create mapping