Preferred Name |
capillary leak syndrome |
|
Synonyms |
idiopathic capillary leak syndrome capillary leak syndrome Capillary Leak Syndrome capillary hyperpermeability syndrome systemic capillary leak syndrome Capillary leak syndrome (disorder) acute vascular leak syndrome Clarkson disease AVLS CLS SCLS periodic systemic capillary leak syndrome capillary leak syndrome with monoclonal gammopathy |
|
Definitions |
A syndrome characterized by leakage of intravascular fluids into the extravascular space. This syndrome is observed in patients who demonstrate a state of generalized leaky capillaries following shock syndromes, low-flow states, ischemia-reperfusion injuries, toxemias, medications, or poisoning. It can lead to generalized edema and multiple organ failure. A condition characterized by recurring episodes of fluid leaking from capillaries into extra-vascular compartments causing hematocrit to rise precipitously. If not treated, generalized vascular leak can lead to generalized EDEMA; SHOCK; cardiovascular collapse; and MULTIPLE ORGAN FAILURE. |
|
ID |
http://www.ebi.ac.uk/efo/EFO_1001284 |
|
closeMatch | ||
database_cross_reference |
NCIt:C62578 UMLS:C0343084 NCIT:C62578 SCTID:87730004 SNOMEDCT:87730004 MESH:D019559 Orphanet:188 MedDRA:10007196 MeSH:D019559 DOID:14400 GARD:1084 ICD9:448.9 MONDO:0001956 |
|
definition |
A syndrome characterized by leakage of intravascular fluids into the extravascular space. This syndrome is observed in patients who demonstrate a state of generalized leaky capillaries following shock syndromes, low-flow states, ischemia-reperfusion injuries, toxemias, medications, or poisoning. It can lead to generalized edema and multiple organ failure. A condition characterized by recurring episodes of fluid leaking from capillaries into extra-vascular compartments causing hematocrit to rise precipitously. If not treated, generalized vascular leak can lead to generalized EDEMA; SHOCK; cardiovascular collapse; and MULTIPLE ORGAN FAILURE. |
|
exactMatch |
http://identifiers.org/snomedct/87730004 http://purl.obolibrary.org/obo/DOID_14400 http://identifiers.org/mesh/D019559 http://linkedlifedata.com/resource/umls/id/C0343084 |
|
has_exact_synonym |
idiopathic capillary leak syndrome capillary leak syndrome Capillary Leak Syndrome capillary hyperpermeability syndrome systemic capillary leak syndrome Capillary leak syndrome (disorder) acute vascular leak syndrome Clarkson disease AVLS CLS SCLS |
|
has_related_synonym |
periodic systemic capillary leak syndrome capillary leak syndrome with monoclonal gammopathy |
|
id |
EFO:1001284 |
|
in_subset |
http://purl.obolibrary.org/obo/mondo/mondo-base#rare http://purl.obolibrary.org/obo/mondo/mondo-base#otar http://purl.obolibrary.org/obo/mondo/mondo-base#gard_rare http://purl.obolibrary.org/obo/mondo/mondo-base#orphanet_rare http://purl.obolibrary.org/obo/mondo/mondo-base#ordo_disease |
|
label |
capillary leak syndrome |
|
notation |
EFO:1001284 |
|
prefLabel |
capillary leak syndrome |
|
term editor |
Sirarat Sarntivijai |
|
subClassOf |