Preferred Name

capillary leak syndrome

Synonyms

CLS

capillary leak syndrome

capillary hyperpermeability syndrome

acute vascular leak syndrome

systemic capillary leak syndrome

idiopathic capillary leak syndrome

Clarkson disease

AVLS

SCLS

capillary leak syndrome with monoclonal gammopathy

periodic systemic capillary leak syndrome

Definitions

A syndrome characterized by leakage of intravascular fluids into the extravascular space. This syndrome is observed in patients who demonstrate a state of generalized leaky capillaries following shock syndromes, low-flow states, ischemia-reperfusion injuries, toxemias, medications, or poisoning. It can lead to generalized edema and multiple organ failure.

ID

http://purl.obolibrary.org/obo/MONDO_0001956

has_exact_synonym

CLS

capillary leak syndrome

capillary hyperpermeability syndrome

acute vascular leak syndrome

systemic capillary leak syndrome

idiopathic capillary leak syndrome

Clarkson disease

AVLS

SCLS

has_related_synonym

capillary leak syndrome with monoclonal gammopathy

periodic systemic capillary leak syndrome

label

capillary leak syndrome

prefixIRI

MONDO:0001956

prefLabel

capillary leak syndrome

textual definition

A syndrome characterized by leakage of intravascular fluids into the extravascular space. This syndrome is observed in patients who demonstrate a state of generalized leaky capillaries following shock syndromes, low-flow states, ischemia-reperfusion injuries, toxemias, medications, or poisoning. It can lead to generalized edema and multiple organ failure.

subClassOf

http://purl.obolibrary.org/obo/MONDO_0001574

http://purl.obolibrary.org/obo/MONDO_0002254

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