Preferred Name | bronchiectasis | |
Synonyms |
Polynesian bronchiectasis |
|
Definitions |
A bronchial disease that is a chronic inflammatory condition of one or more bronchi or bronchioles marked by dilatation and loss of elasticity of the walls resulting from damage to the airway wall leading to the formation of small sacs on the bronchial wall and impairment of cilia mobility in the lung. Inflammation of the bronchial wall increases mucus secretion which serves as a breeding ground for bacteria. Bronchiectasis is caused by repeated respiratory infections, immune deficiency disorders, hereditary disorders (cystic fibrosis or primary ciliary dyskinesia), mechanical factors (inhaled object or a lung tumor) or inhaling toxic substances. Xref MGI. OMIM mapping confirmed by DO. [SN]. |
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ID |
http://purl.obolibrary.org/obo/DOID_9563 |
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comment |
Xref MGI. OMIM mapping confirmed by DO. [SN]. |
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alternative label |
Polynesian bronchiectasis |
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database_cross_reference |
ICD10CM:J47 SNOMEDCT_US_2023_03_01:155580000 MIM:PS211400 MESH:D001987 UMLS_CUI:C0006267 ICD9CM:494 MIM:211400 MIM:613021 MIM:613071 NCI:C84475 ORDO:60033 |
|
definition |
A bronchial disease that is a chronic inflammatory condition of one or more bronchi or bronchioles marked by dilatation and loss of elasticity of the walls resulting from damage to the airway wall leading to the formation of small sacs on the bronchial wall and impairment of cilia mobility in the lung. Inflammation of the bronchial wall increases mucus secretion which serves as a breeding ground for bacteria. Bronchiectasis is caused by repeated respiratory infections, immune deficiency disorders, hereditary disorders (cystic fibrosis or primary ciliary dyskinesia), mechanical factors (inhaled object or a lung tumor) or inhaling toxic substances. |
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has exact synonym |
Polynesian bronchiectasis |
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has_alternative_id |
DOID:11046 DOID:11047 DOID:9571 |
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has_obo_namespace |
disease_ontology |
|
id |
DOID:9563 |
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in_subset | ||
label |
bronchiectasis |
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notation |
DOID:9563 |
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prefLabel |
bronchiectasis |
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subClassOf |