STO

Last uploaded: November 28, 2017
Preferred Name

Moyamoya disease

Synonyms
ID

http://www.semanticweb.org/ontologies/STO.owl#OWLClass_901b7fda_765b_41eb_83ba_c61dab4de81d

hasDbXref

MIM: 252350

http://purl.bioontology.org/ontology/SNOMEDCT/69116000

isDefinedBy

Moyamoya syndrome is a disease in which certain arteries in the brain are constricted. Blood flow is blocked by the constriction, and also by blood clots.

MOYAMOYA, a Japanese word meaning "something hazy like a puff of cigarette smoke drifting in the air,''is the descriptive term we apply to a peculiar angiographic picture consisting of abnormal net-like vessels at the base of the brain. In addition to this abnormality, angiography usually reveals stenosis or occlusion of the internal carotid artery at the level of its terminal bifurcation together with abnormalities of the anterior and middle cerebral arteries. These changes are usually bilateral.

label

Moyamoya disease

prefixIRI

OWLClass_901b7fda_765b_41eb_83ba_c61dab4de81d

prefLabel

Moyamoya disease

references

Scott, R. M., & Smith, E. R. (2009). Moyamoya disease and moyamoya syndrome. New England Journal of Medicine, 360(12), 1226-1237.

resource

Suzuki, J. I. R. O., & Kodama, N. A. M. I. O. (1983). Moyamoya disease--a review. Stroke, 14(1), 104-109.

source

Merritt, H. H. (2010). Merritt's neurology. L. P. Rowland, & T. A. Pedley (Eds.). Lippincott Williams & Wilkins.

synonyms

Familial moyamoya disease

Moyamoya syndrome

MMD

subClassOf

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http://www.semanticweb.org/ontologies/STO.owl#OWLClass_58b4258a_2a57_416d_a501_aae8cbe606e7

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