Preferred Name |
Primary Biliary Cirrhosis |
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Synonyms |
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ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Primary_Biliary_Cirrhosis |
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DEFINITION |
An autoimmune inflammatory disorder characterized by destruction of the small intrahepatic bile ducts. It affects predominantly females and it may lead to cirrhosis and liver failure. Patients have antimitochondrial and antinuclear antibodies in the peripheral blood. |
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FULL_SYN |
Chronic Non-Suppurative Destructive Cholangitis Primary Bilary Cirrhosis (PBC) |
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isDefinedBy |
An autoimmune inflammatory disorder characterized by destruction of the small intrahepatic bile ducts. It affects predominantly females and it may lead to cirrhosis and liver failure. Patients have antimitochondrial and antinuclear antibodies in the peripheral blood. |
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label |
Primary Biliary Cirrhosis |
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prefixIRI |
Thesaurus:Primary_Biliary_Cirrhosis |
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prefLabel |
Primary Biliary Cirrhosis |
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Synonym |
Chronic Non-Suppurative Destructive Cholangitis Primary Bilary Cirrhosis (PBC) |
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subClassOf |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Biliary_Cirrhosis |