Preferred Name |
Aggressive Systemic Mastocytosis |
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Synonyms |
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ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Aggressive_Systemic_Mastocytosis |
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DEFINITION |
An aggressive and progressive mast cell neoplasm characterized by systemic infiltration of internal organs by aggregates of neoplastic mast cells. There is no evidence of mast cell leukemia or clonal hematologic malignancy. Clinical symptoms include hepatomegaly, splenomegaly, portal hypertension, malabsorption syndrome, and pathologic fractures. |
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FULL_SYN |
ASM |
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isDefinedBy |
An aggressive and progressive mast cell neoplasm characterized by systemic infiltration of internal organs by aggregates of neoplastic mast cells. There is no evidence of mast cell leukemia or clonal hematologic malignancy. Clinical symptoms include hepatomegaly, splenomegaly, portal hypertension, malabsorption syndrome, and pathologic fractures. |
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label |
Aggressive Systemic Mastocytosis |
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prefixIRI |
Thesaurus:Aggressive_Systemic_Mastocytosis |
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prefLabel |
Aggressive Systemic Mastocytosis |
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Synonym |
ASM |
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subClassOf |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Primary_Systemic_Mastocytosis http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Malignant_Mastocytosis |