Preferred Name | hemophagocytic syndrome | |
Synonyms |
"HPS" EXACT [] "haemophagocytic syndrome" EXACT [] |
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Definitions |
"A syndrome that is characterized by an expansion of the monocyte-macrophage population and intense hemophagocytosis. It can occur de novo, but more often occurs in the setting of another disorder, usually an infection or a malignancy. A clinical picture of fever, hepatosplenomegaly, lymphadenopathy and peripheral pancytopenia. The morphologic hallmark of this syndrome is the phagocytosis of hematopoietic elements by morphologically normal macrophages." [url:http\://www.mayoclinicproceedings.com/inside.asp?AID=57&UID=, url:http\://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31801997000500007&lng=pt&nrm=iso] |
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ID |
http://purl.obolibrary.org/obo/DOID_0050120 |
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comment |
"A syndrome that is characterized by an expansion of the monocyte-macrophage population and intense hemophagocytosis. It can occur de novo, but more often occurs in the setting of another disorder, usually an infection or a malignancy. A clinical picture of fever, hepatosplenomegaly, lymphadenopathy and peripheral pancytopenia. The morphologic hallmark of this syndrome is the phagocytosis of hematopoietic elements by morphologically normal macrophages." [url:http\://www.mayoclinicproceedings.com/inside.asp?AID=57&UID=, url:http\://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31801997000500007&lng=pt&nrm=iso] |
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alternative term |
"HPS" EXACT [] "haemophagocytic syndrome" EXACT [] |
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label |
hemophagocytic syndrome |
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prefixIRI |
DOID:0050120 |
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prefLabel |
hemophagocytic syndrome |
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see also | ||
subClassOf |