loading...| Preferred Name |
Aggressive Systemic Mastocytosis |
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| Synonyms |
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| Definitions |
An aggressive and progressive mast cell neoplasm characterized by systemic infiltration of internal organs by aggregates of neoplastic mast cells. There is no evidence of mast cell leukemia or clonal hematologic malignancy. Clinical symptoms include hepatomegaly, splenomegaly, portal hypertension, malabsorption syndrome, and pathologic fractures. |
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| ID |
http://purl.obolibrary.org/obo/NCIT_C9285 |
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| code |
C9285 |
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| Contributing_Source |
CTRP GDC |
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| definition |
An aggressive and progressive mast cell neoplasm characterized by systemic infiltration of internal organs by aggregates of neoplastic mast cells. There is no evidence of mast cell leukemia or clonal hematologic malignancy. Clinical symptoms include hepatomegaly, splenomegaly, portal hypertension, malabsorption syndrome, and pathologic fractures. |
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| Display_Name |
Aggressive Systemic Mastocytosis |
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| ICD-O-3_Code |
9741/3 |
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| in_subset |
http://purl.obolibrary.org/obo/NCIT_C177537 http://purl.obolibrary.org/obo/NCIT_C116977 http://purl.obolibrary.org/obo/NCIT_C126659 |
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| Is_Value_For_GDC_Property | ||
| label |
Aggressive Systemic Mastocytosis |
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| Legacy Concept Name |
Aggressive_Systemic_Mastocytosis |
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| Maps_To |
Aggressive systemic mastocytosis 9741/3 |
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| Neoplastic_Status |
Malignant |
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| Preferred_Name |
Aggressive Systemic Mastocytosis |
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| prefixIRI |
NCIT:C9285 |
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| prefLabel |
Aggressive Systemic Mastocytosis |
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| Semantic_Type |
Neoplastic Process |
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| UMLS_CUI |
C1112486 |
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| subClassOf |