Preferred Name | Scleroderma | |
Synonyms |
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Definitions |
A localized or systemic chronic and progressive autoimmune disorder characterized by thickening of the skin and the connective tissues. Localized scleroderma affects only the skin. Systemic scleroderma affects internal organs, including the heart, lungs, gastrointestinal tract, and kidneys. |
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ID |
http://purl.obolibrary.org/obo/NCIT_C26746 |
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ALT_DEFINITION |
A chronic and progressive autoimmune disorder characterized by thickening of the skin and the connective tissues. A chronic disorder marked by hardening and thickening of the skin. Scleroderma can be localized or it can affect the entire body (systemic). |
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code |
C26746 |
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Contributing_Source |
FDA MedDRA NICHD PCDC |
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definition |
A localized or systemic chronic and progressive autoimmune disorder characterized by thickening of the skin and the connective tissues. Localized scleroderma affects only the skin. Systemic scleroderma affects internal organs, including the heart, lungs, gastrointestinal tract, and kidneys. |
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FDA_Table |
Patient Code (Appendix B) |
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in_subset |
http://purl.obolibrary.org/obo/NCIT_C90259 http://purl.obolibrary.org/obo/NCIT_C186341 |
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label |
Scleroderma |
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Legacy Concept Name |
Scleroderma |
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Maps_To |
Scleroderma |
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Preferred_Name |
Scleroderma |
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prefixIRI |
NCIT:C26746 |
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prefLabel |
Scleroderma |
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Semantic_Type |
Disease or Syndrome |
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UMLS_CUI |
C0011644 |
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subClassOf |