loading...| Preferred Name |
Pemphigus erythematosus |
|
| Synonyms |
Senear-Usher syndrome |
|
| Definitions |
A rare superficial pemphigus disease characterized clinically by well-demarcated, localized, erythematous, scaly, hyperkeratotic, crusted plaques, with frequent butterfly distribution over the malar area of the face (but also commonly involving trunk and scalp, and less frequently the extremities, with a photoexposed distribution). Histologically, granular deposits along the dermal-epidermal junction, in addition to intercellular deposition in the upper epidermis, are observed. |
|
| ID |
http://www.orpha.net/ORDO/Orphanet_79480 |
|
| alternative_term |
Senear-Usher syndrome Seborrheic pemphigus |
|
| definition |
A rare superficial pemphigus disease characterized clinically by well-demarcated, localized, erythematous, scaly, hyperkeratotic, crusted plaques, with frequent butterfly distribution over the malar area of the face (but also commonly involving trunk and scalp, and less frequently the extremities, with a photoexposed distribution). Histologically, granular deposits along the dermal-epidermal junction, in addition to intercellular deposition in the upper epidermis, are observed. |
|
| definition_citation |
Orphanet |
|
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=79480 |
|
| hasDbXref |
UMLS:C0263312 ICD-11:EB40.1 MedDRA:10058917 ICD-10:L10.4 |
|
| label |
Pemphigus erythematosus |
|
| notation |
ORPHA:79480 |
|
| part_of | ||
| prefixIRI |
ORDO:Orphanet_79480 |
|
| prefLabel |
Pemphigus erythematosus |
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| treeView | ||
| subClassOf |