Preferred Name |
Rare cutaneous lupus erythematosus |
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Synonyms |
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Definitions |
Rare cutaneous lupus erythematosus (CLE) is an autoimmune disease that denotes a heterogeneous spectrum of clinical manifestations affecting the skin and can be divided into 4 categories: acute CLE (ACLE); subacute CLE (SCLE); chronic CLE (CCLE; the most diverse form); and intermittent CLE (ICLE). CLE can either occur alone or associated with systemic lupus erythematosus (SLE). |
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ID |
http://www.orpha.net/ORDO/Orphanet_535 |
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definition |
Rare cutaneous lupus erythematosus (CLE) is an autoimmune disease that denotes a heterogeneous spectrum of clinical manifestations affecting the skin and can be divided into 4 categories: acute CLE (ACLE); subacute CLE (SCLE); chronic CLE (CCLE; the most diverse form); and intermittent CLE (ICLE). CLE can either occur alone or associated with systemic lupus erythematosus (SLE). |
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definition_citation |
Orphanet |
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expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=535 |
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has_age_of_onset |
All ages |
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has_inheritance |
Multigenic/multifactorial |
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hasDbXref |
UMLS:C5680424 MedDRA:10056509 |
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label |
Rare cutaneous lupus erythematosus |
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notation |
Clinical group ORPHA:535 |
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prefixIRI |
ORDO:Orphanet_535 |
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prefLabel |
Rare cutaneous lupus erythematosus |
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present_in |
United States AND has_annual_incidence_average_value : 4.3 AND has_annual_incidence_range : 1-9 / 100 000 Europe AND has_point_prevalence_average_value : 50.0 AND has_point_prevalence_range : 1-5 / 10 000 Sweden AND has_annual_incidence_average_value : 4.0 AND has_annual_incidence_range : 1-9 / 100 000 United States AND has_point_prevalence_average_value : 73.0 AND has_point_prevalence_range : 6-9 / 10 000 |
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subClassOf |