Preferred Name

Anti-Glomerular Basement Membrane Disease [Disease/Finding]

Synonyms

Goodpasture Syndrome

ID

http://purl.bioontology.org/ontology/NDFRT/N0000003962

altLabel

Goodpasture Syndrome

Anti-GBM Disease

Goodpasture's Syndrome

Lung Purpura with Nephritis

Anti-Glomerular Basement Membrane Disease

cui

C0403529

MESH DEFINITION

An autoimmune disease of the KIDNEY and the LUNG. It is characterized by the presence of circulating autoantibodies targeting the epitopes in the non-collagenous domains of COLLAGEN TYPE IV in the basement membranes of kidney glomeruli (KIDNEY GLOMERULUS) and lung alveoli (PULMONARY ALVEOLI), and the subsequent destruction of these basement membranes. Clinical features include pulmonary alveolar hemorrhage and glomerulonephritis.

MESH DUI

D019867

MeSH name

Anti-Glomerular Basement Membrane Disease

MESH UI

M0029493

NDFRT kind

DISEASE_KIND

notation

N0000003962

NUI

N0000003962

prefLabel

Anti-Glomerular Basement Membrane Disease [Disease/Finding]

SNOMED CID

236506009

tui

T047

subClassOf

http://purl.bioontology.org/ontology/NDFRT/N0000000514

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/ICD9CM/446.21 ICD9CM CUI
http://purl.bioontology.org/ontology/SNOMEDCT/788613004 SNOMEDCT CUI
http://purl.bioontology.org/ontology/WHO/1464 WHO-ART CUI
http://purl.bioontology.org/ontology/SCTSPA/50581000 SCTSPA CUI
http://purl.bioontology.org/ontology/CST/GLOMERULITIS COSTART CUI
http://purl.bioontology.org/ontology/RCD/X30Kz RCD CUI
http://purl.bioontology.org/ontology/MDRFRE/10018620 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10081981 MEDDRA CUI
http://purl.bioontology.org/ontology/MEDDRA/10042811 MEDDRA CUI
http://purl.bioontology.org/ontology/SCTSPA/788613004 SCTSPA CUI
http://purl.bioontology.org/ontology/MDRFRE/10081981 MDRFRE CUI
http://purl.bioontology.org/ontology/CSP/0944-7918 CRISP CUI
http://purl.bioontology.org/ontology/MESH/D019867 MESH CUI
http://purl.bioontology.org/ontology/ICD10CM/M31.0 ICD10CM CUI
http://purl.bioontology.org/ontology/MEDDRA/10081982 MEDDRA CUI
http://purl.bioontology.org/ontology/MDRFRE/10081982 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10018620 MEDDRA CUI
http://purl.bioontology.org/ontology/MDRGER/10081981 MDRGER CUI
http://purl.bioontology.org/ontology/MSHFRE/D019867 MSHFRE CUI
http://purl.bioontology.org/ontology/MDRGER/10042811 MDRGER CUI
http://purl.bioontology.org/ontology/OMIM/233450 OMIM CUI
http://purl.bioontology.org/ontology/MDRGER/10018620 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10081982 MDRGER CUI
http://purl.bioontology.org/ontology/WHOFRE/1464 WHOFRE CUI
http://purl.bioontology.org/ontology/MDRFRE/10042811 MDRFRE CUI
http://purl.bioontology.org/ontology/SNMI/D7-12340 SNMI CUI
http://purl.bioontology.org/ontology/SNOMEDCT/50581000 SNOMEDCT CUI
http://purl.bioontology.org/ontology/RCD/G7520 RCD CUI