Preferred Name

Histiocytosis, Langerhans-Cell [Disease/Finding]

Synonyms

Histiocytosis X

ID

http://purl.bioontology.org/ontology/NDFRT/N0000001544

altLabel

Histiocytosis X

Letterer-Siwe Disease

Hand-Schüller-Christian Disease

Histiocytosis-X

Histiocytosis, Generalized

Type 2 Histiocytosis

Hand-Schueller-Christian Syndrome

Non-Lipid Reticuloendotheliosis

Histiocytosis, Langerhans-Cell

Hand-Schueller-Christian Disease

Langerhans Cell Histiocytosis

Systemic Aleukemic Reticuloendotheliosis

Langerhans-Cell Histiocytosis

Langerhans-Cell Granulomatosis

Langerhans Cell Granulomatosis

Hand-Schüller-Christian Syndrome

Schueller-Christian Disease

cui

C0019621

May be treated by

http://purl.bioontology.org/ontology/NDFRT/N0000161190

http://purl.bioontology.org/ontology/NDFRT/N0000164307

http://purl.bioontology.org/ontology/NDFRT/N0000148588

http://purl.bioontology.org/ontology/NDFRT/N0000177389

http://purl.bioontology.org/ontology/NDFRT/N0000164308

MESH DEFINITION

A group of disorders resulting from the abnormal proliferation of and tissue infiltration by LANGERHANS CELLS which can be detected by their characteristic Birbeck granules (X bodies), or by monoclonal antibody staining for their surface CD1 ANTIGENS. Langerhans-cell granulomatosis can involve a single organ, or can be a systemic disorder.

MESH DUI

D006646

MeSH name

Histiocytosis, Langerhans-Cell

MESH UI

M0010406

NDFRT kind

DISEASE_KIND

notation

N0000001544

NUI

N0000001544

prefLabel

Histiocytosis, Langerhans-Cell [Disease/Finding]

SNOMED CID

190955000

190956004

65399007

tui

T191

subClassOf

http://purl.bioontology.org/ontology/NDFRT/N0000003294

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/MEDDRA/10053133 MEDDRA CUI
http://purl.bioontology.org/ontology/ICD10CM/C96.6 ICD10CM CUI
http://purl.bioontology.org/ontology/SCTSPA/110450007 SCTSPA CUI
http://purl.bioontology.org/ontology/SNOMEDCT/65399007 SNOMEDCT CUI
http://purl.bioontology.org/ontology/CSP/0427-5330 CRISP CUI
http://purl.bioontology.org/ontology/PDQ/CDR0000641624 PDQ CUI
http://purl.bioontology.org/ontology/SCTSPA/65399007 SCTSPA CUI
http://purl.bioontology.org/ontology/MDRFRE/10069698 MDRFRE CUI
http://purl.bioontology.org/ontology/MESH/D006646 MESH CUI
http://purl.bioontology.org/ontology/MEDDRA/10069698 MEDDRA CUI
http://purl.bioontology.org/ontology/OMIM/604856 OMIM CUI
http://purl.bioontology.org/ontology/MDRFRE/10023688 MDRFRE CUI
http://purl.bioontology.org/ontology/MDRFRE/10053133 MDRFRE CUI
http://purl.bioontology.org/ontology/MSHFRE/D006646 MSHFRE CUI
http://purl.bioontology.org/ontology/SNOMEDCT/110450007 SNOMEDCT CUI
http://purl.bioontology.org/ontology/PDQ/CDR0000039054 PDQ CUI
http://purl.bioontology.org/ontology/MDRGER/10023688 MDRGER CUI
http://purl.bioontology.org/ontology/RCD/X20E9 RCD CUI
http://purl.bioontology.org/ontology/MDRGER/10053133 MDRGER CUI
http://purl.bioontology.org/ontology/RCD/C37y5 RCD CUI
http://purl.bioontology.org/ontology/SNMI/D6-64952 SNMI CUI
http://purl.bioontology.org/ontology/MEDDRA/10023688 MEDDRA CUI
http://purl.bioontology.org/ontology/MDRGER/10069698 MDRGER CUI
http://evs.nci.nih.gov/ftp1/NDF-RT/NDF-RT.owl#N0000001544 ODAE LOOM