Preferred Name |
Sezary Syndrome |
|
Synonyms |
Sezary disease Sezary syndrome Sezary Syndrome Sezary disease, unspecified site Cutaneous T-cell lymphoma/Sezary syndrome CTCL / Sezary syndrome Sezary's Disease Sézary Syndrome |
|
Definitions |
A generalized peripheral (mature) T-cell neoplasm characterized by the presence of erythroderma, lymphadenopathy, and neoplastic, cerebriform T-lymphocytes in the blood. Sezary syndrome is an aggressive disease. (WHO, 2001) |
|
ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3366 |
|
ALT_DEFINITION |
A form of cutaneous T-cell lymphoma, a cancerous disease that affects the skin. |
|
code |
C3366 |
|
Concept_In_Subset |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C157711 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C156952 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168661 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168656 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168662 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193175 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C156966 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C116977 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168658 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193248 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C192842 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C126659 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C118168 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C165258 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C103133 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C102905 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193231 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193006 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C168655 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C158520 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C193249 |
|
Contributing_Source |
Cellosaurus CPTAC CTEP CTRP GDC mCode |
|
DEFINITION |
A generalized peripheral (mature) T-cell neoplasm characterized by the presence of erythroderma, lymphadenopathy, and neoplastic, cerebriform T-lymphocytes in the blood. Sezary syndrome is an aggressive disease. (WHO, 2001) |
|
Display_Name |
Sezary Syndrome |
|
FULL_SYN |
Sezary disease Sezary syndrome Sezary Syndrome Sezary disease, unspecified site Cutaneous T-cell lymphoma/Sezary syndrome CTCL / Sezary syndrome Sezary's Disease Sézary Syndrome |
|
ICD-O-3_Code |
9701/3 |
|
Is_Value_For_GDC_Property | ||
label |
Sezary Syndrome |
|
Legacy Concept Name |
Sezary_Syndrome |
|
Maps_To |
Sezary disease Sezary syndrome Sezary disease, unspecified site 9701/3 |
|
Neoplastic_Status |
Malignant |
|
Preferred_Name |
Sezary Syndrome |
|
prefixIRI |
Thesaurus:C3366 |
|
Semantic_Type |
Neoplastic Process |
|
UMLS_CUI |
C0036920 |
|
subClassOf |