Preferred Name |
Hearing Loss, Central
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Synonyms |
Deafness, Cortical
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Definitions |
Hearing loss due to disease of the AUDITORY PATHWAYS (in the CENTRAL NERVOUS SYSTEM) which originate in the COCHLEAR NUCLEI of the PONS and then ascend bilaterally to the MIDBRAIN, the THALAMUS, and then the AUDITORY CORTEX in the TEMPORAL LOBE. Bilateral lesions of the auditory pathways are usually required to cause central hearing loss. Cortical deafness refers to loss of hearing due to bilateral auditory cortex lesions. Unilateral BRAIN STEM lesions involving the cochlear nuclei may result in unilateral hearing loss.
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ID |
http://purl.bioontology.org/ontology/MESH/D006313
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altLabel |
Deafness, Cortical Central Hearing Loss Cortical Deafness
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AN |
coordinate with VESTIBULOCOCHLEAR NERVE DISEASES for hearing loss due to cochlear nerve disease
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AQL |
BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI
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cui |
C0392704 C0018776
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DC |
1
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definition |
Hearing loss due to disease of the AUDITORY PATHWAYS (in the CENTRAL NERVOUS SYSTEM) which originate in the COCHLEAR NUCLEI of the PONS and then ascend bilaterally to the MIDBRAIN, the THALAMUS, and then the AUDITORY CORTEX in the TEMPORAL LOBE. Bilateral lesions of the auditory pathways are usually required to cause central hearing loss. Cortical deafness refers to loss of hearing due to bilateral auditory cortex lesions. Unilateral BRAIN STEM lesions involving the cochlear nuclei may result in unilateral hearing loss.
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DX |
19910101
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FX |
D000160
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HN |
91(79); was see under HEARING LOSS, SENSORINEURAL 1979-90
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Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000178 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000469 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000209 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000523 http://purl.bioontology.org/ontology/MESH/Q000401
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Inverse of RO |
http://purl.bioontology.org/ontology/MESH/D000160
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Machine permutation |
91; was see under HEARING LOSS, SENSORINEURAL 1979-90
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Mapped from |
http://purl.bioontology.org/ontology/MESH/C538203 http://purl.bioontology.org/ontology/MESH/C538205 http://purl.bioontology.org/ontology/MESH/C538202 http://purl.bioontology.org/ontology/MESH/C538200 http://purl.bioontology.org/ontology/MESH/C538201 http://purl.bioontology.org/ontology/MESH/C537568 http://purl.bioontology.org/ontology/MESH/C537192 http://purl.bioontology.org/ontology/MESH/C537305 http://purl.bioontology.org/ontology/MESH/C537476 http://purl.bioontology.org/ontology/MESH/C537129 http://purl.bioontology.org/ontology/MESH/C565640 http://purl.bioontology.org/ontology/MESH/C564769 http://purl.bioontology.org/ontology/MESH/C538268 http://purl.bioontology.org/ontology/MESH/C563790 http://purl.bioontology.org/ontology/MESH/C535996 http://purl.bioontology.org/ontology/MESH/C537235
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MDA |
19780522
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MMR |
20200303
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MN |
C09.218.458.341.887.432 C23.888.592.763.393.341.887.432 C10.597.751.418.341.887.432 C09.218.807.186.432 C10.228.140.068.432
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notation |
D006313
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prefLabel |
Hearing Loss, Central
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TERMUI |
T019137 T363969 T363967 T363968
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TH |
NLM (1979) NLM (2000)
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tui |
T047
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subClassOf |
http://purl.bioontology.org/ontology/MESH/D001304 http://purl.bioontology.org/ontology/MESH/D006319
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