Preferred Name |
Waldenstrom Macroglobulinemia |
|
Synonyms |
Familial Waldenstroms Macroglobulinaemia |
|
Definitions |
A lymphoproliferative disorder characterized by pleomorphic B-LYMPHOCYTES including PLASMA CELLS, with increased levels of monoclonal serum IMMUNOGLOBULIN M. There is lymphoplasmacytic cells infiltration into bone marrow and often other tissues, also known as lymphoplasmacytic lymphoma. Clinical features include ANEMIA; HEMORRHAGES; and hyperviscosity. |
|
ID |
http://purl.bioontology.org/ontology/MESH/D008258 |
|
altLabel |
Familial Waldenstroms Macroglobulinaemia Waldenstrom Macroglobulinaemia Lymphoplasmacytoid Lymphoma Lymphomas, Lymphoplasmacytoid Macroglobulinaemia, Familial Waldenstrom's Macroglobulinemia Primary Macroglobulinemia Lymphoplasmacytoid Lymphomas Lymphoma, Lymphocytic, Plasmacytoid Waldenstrom's Macroglobulinemia Macroglobulinemia, Waldenstrom's Macroglobulinemia, Primary Macroglobulinemia, Waldenstrom Waldenstroms Macroglobulinaemia Waldenstroms Macroglobulinemia Waldenstrom's Macroglobulinaemia Macroglobulinaemia, Waldenstrom's Lymphoma, Lymphoplasmacytoid Familial Waldenstrom Macroglobulinaemia Waldenstrom's Macroglobulinaemia, Familial Familial Waldenstrom's Macroglobulinaemia |
|
AN |
in titles & translations use diacritic: Waldenström |
|
AQL |
BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI |
|
cui |
C0024419 C2936755 |
|
DC |
1 |
|
definition |
A lymphoproliferative disorder characterized by pleomorphic B-LYMPHOCYTES including PLASMA CELLS, with increased levels of monoclonal serum IMMUNOGLOBULIN M. There is lymphoplasmacytic cells infiltration into bone marrow and often other tissues, also known as lymphoplasmacytic lymphoma. Clinical features include ANEMIA; HEMORRHAGES; and hyperviscosity. |
|
DX |
19990101 |
|
HN |
1999 (1963) |
|
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000178 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000469 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000209 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000652 |
|
Machine permutation |
1999; see WALDENSTROM'S MACROGLOBULINEMIA 1992-98, see MACROGLOBULINEMIA 1963-91; for LYMPHOMA, LYMPHOCYTIC, PLASMACYTOID see LYMPHOMA, SMALL CELL 1991-2007 |
|
MDA |
19990101 |
|
MMR |
20100625 |
|
MN |
C15.604.515.925 C15.378.147.780.925 C15.378.463.515.960 C14.907.454.960 C20.683.780.925 C04.557.595.925 |
|
notation |
D008258 |
|
prefLabel |
Waldenstrom Macroglobulinemia |
|
TERMUI |
T024635 T768342 T680470 T024637 T024636 T024507 T684225 T768343 |
|
TH |
NLM (1999) NLM (1991) NLM (1966) NLM (2008) NLM (1992) NLM (2011) ORD (2010) |
|
tui |
T191 |
|
subClassOf |
http://purl.bioontology.org/ontology/MESH/D020141 http://purl.bioontology.org/ontology/MESH/D008232 |