Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Kuru

Synonyms

Kuru Encephalopathy

Definitions

A prion disease found exclusively among the Fore linguistic group natives of the highlands of NEW GUINEA. The illness is primarily restricted to adult females and children of both sexes. It is marked by the subacute onset of tremor and ataxia followed by motor weakness and incontinence. Death occurs within 3-6 months of disease onset. The condition is associated with ritual cannibalism, and has become rare since this practice has been discontinued. Pathologic features include a noninflammatory loss of neurons that is most prominent in the cerebellum, glial proliferation, and amyloid plaques. (From Adams et al., Principles of Neurology, 6th ed, p773)

ID

http://purl.bioontology.org/ontology/MESH/D007729

altLabel

Kuru Encephalopathy

Encephalopathy, Kuru

AN

do not confuse with KORO, a depersonalization disord

AQL

BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH TM UR VE VI

cui

C0022802

DC

1

definition

A prion disease found exclusively among the Fore linguistic group natives of the highlands of NEW GUINEA. The illness is primarily restricted to adult females and children of both sexes. It is marked by the subacute onset of tremor and ataxia followed by motor weakness and incontinence. Death occurs within 3-6 months of disease onset. The condition is associated with ritual cannibalism, and has become rare since this practice has been discontinued. Pathologic features include a noninflammatory loss of neurons that is most prominent in the cerebellum, glial proliferation, and amyloid plaques. (From Adams et al., Principles of Neurology, 6th ed, p773)

DX

19660101

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000635

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000382

MDA

19990101

MMR

20190617

MN

C10.228.228.800.435

C01.207.800.435

C10.574.843.625

notation

D007729

prefLabel

Kuru

TERMUI

T023178

T368848

T368847

TH

NLM (2000)

NLM (1966)

tui

T047

subClassOf

http://purl.bioontology.org/ontology/MESH/D017096

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http://purl.bioontology.org/ontology/MDRGER/10023497 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10023498 MDRGER CUI
http://purl.bioontology.org/ontology/CSP/2042-5006 CRISP CUI
http://purl.bioontology.org/ontology/MEDDRA/10023497 MEDDRA CUI
http://purl.bioontology.org/ontology/NDFRT/N0000001765 NDFRT CUI
http://purl.bioontology.org/ontology/MSHFRE/D007729 MSHFRE CUI
http://purl.bioontology.org/ontology/MDRFRE/10023498 MDRFRE CUI
http://purl.bioontology.org/ontology/SNMI/DE-3B010 SNMI CUI
http://purl.bioontology.org/ontology/RCD/A410. RCD CUI
http://purl.bioontology.org/ontology/MEDDRA/10023498 MEDDRA CUI
http://purl.bioontology.org/ontology/MDRFRE/10023497 MDRFRE CUI
http://purl.bioontology.org/ontology/SNOMEDCT/86188000 SNOMEDCT CUI
http://purl.bioontology.org/ontology/ICD9CM/046.0 ICD9CM CUI
http://purl.bioontology.org/ontology/ICD10CM/A81.81 ICD10CM CUI
http://purl.bioontology.org/ontology/SCTSPA/86188000 SCTSPA CUI
http://www.ebi.ac.uk/efo/EFO_1001008 EFO LOOM
http://purl.obolibrary.org/obo/DOID_648 DOID LOOM
http://purl.obolibrary.org/obo/MONDO_0006825 MONDO LOOM
http://id.nlm.nih.gov/mesh/D007729 MDM LOOM
http://purl.bioontology.org/ontology/MEDDRA/10023497 MEDDRA LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.228.228.800.435 RH-MESH LOOM
http://purl.obolibrary.org/obo/GAZ_00558006 GAZ LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#7139 OCHV LOOM
http://doe-generated-ontology.com/OntoAD#C0022802 ONTOAD LOOM
http://purl.jp/bio/4/id/200906057075749471 IOBC LOOM
http://localhost/plosthes.2017-1#3825 PLOSTHES LOOM
http://www.phoc.org.cn/pmo/class/PMO_00036061 PMAPP-PMO LOOM
http://purl.obolibrary.org/obo/OMIT_0008832 OMIT LOOM
http://purl.bioontology.org/ontology/SNMI/DE-3B010 SNMI LOOM
http://identifiers.org/omim/245300 REXO LOOM
http://identifiers.org/omim/245300 GEXO LOOM
http://identifiers.org/omim/245300 RETO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D007729 RH-MESH LOOM
http://purl.bioontology.org/ontology/RCD/A410. RCD LOOM
http://purl.obolibrary.org/obo/MONDO_0006825 DOVES LOOM
http://www.orpha.net/ORDO/Orphanet_454745 ORDO LOOM
http://uri.neuinfo.org/nif/nifstd/birnlex_12693 NIFDYS LOOM
http://uri.neuinfo.org/nif/nifstd/birnlex_12693 NIFSTD LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/86188000 SNOMEDCT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.574.843.625 RH-MESH LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0022802 OCHV LOOM
http://bioontology.org/projects/ontologies/birnlex#birnlex_12693 BIRNLEX LOOM
http://purl.bioontology.org/ontology/RCTV2/A410.00 RCTV2 LOOM
http://purl.bioontology.org/ontology/ICD9CM/046.0 ICD9CM LOOM
http://purl.obolibrary.org/obo/OMIM_245300 CCO LOOM
http://purl.bioontology.org/ontology/ICD10CM/A81.81 ICD10CM LOOM
http://purl.obolibrary.org/obo/DOID_648 BAO LOOM
http://purl.obolibrary.org/obo/DOID_648 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_648 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_648 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_648 FNS-H LOOM
http://purl.obolibrary.org/obo/GAZ_00552981 GAZ LOOM
http://purl.obolibrary.org/obo/PW_0000268 PW LOOM