Preferred Name |
Factor XIII |
|
Synonyms |
Transamidase, Factor XIII Blood Coagulation Factor XIII Laki-Lorand Factor Factor XIII Transamidase Laki Lorand Factor Coagulation Factor XIII Fibrin Stabilizing Factor Stabilizing Factor, Fibrin Factor 13 Blood-coagulation factor XIII Fibrinase XIII, Coagulation Factor Factor Thirteen Factor XIII, Coagulation |
|
Definitions |
A fibrin-stabilizing plasma enzyme (TRANSGLUTAMINASES) that is activated by THROMBIN and CALCIUM to form FACTOR XIIIA. It is important for stabilizing the formation of the fibrin polymer (clot) which culminates the coagulation cascade. |
|
ID |
http://purl.bioontology.org/ontology/MESH/D005176 |
|
altLabel |
Transamidase, Factor XIII Blood Coagulation Factor XIII Laki-Lorand Factor Factor XIII Transamidase Laki Lorand Factor Coagulation Factor XIII Fibrin Stabilizing Factor Stabilizing Factor, Fibrin Factor 13 Blood-coagulation factor XIII Fibrinase XIII, Coagulation Factor Factor Thirteen Factor XIII, Coagulation |
|
AN |
activated form use FACTOR XIIIA |
|
AQL |
AA AD AE AG AI AN BI CF CH CL CS DE EC GE HI IM IP ME PD PH PK PO RE SD ST TO TU UL UR |
|
cui |
C0015528 |
|
DC |
1 |
|
definition |
A fibrin-stabilizing plasma enzyme (TRANSGLUTAMINASES) that is activated by THROMBIN and CALCIUM to form FACTOR XIIIA. It is important for stabilizing the formation of the fibrin polymer (clot) which culminates the coagulation cascade. |
|
DX |
19700101 |
|
EC |
deficiency:Factor XIII Deficiency |
|
FX |
D003029 |
|
HN |
1970(1964); for FACTOR XIII TRANSAMIDASE see TRANSGLUTAMINASES (1990-2001) |
|
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000096 http://purl.bioontology.org/ontology/MESH/Q000627 http://purl.bioontology.org/ontology/MESH/Q000648 http://purl.bioontology.org/ontology/MESH/Q000493 http://purl.bioontology.org/ontology/MESH/Q000494 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000138 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000008 http://purl.bioontology.org/ontology/MESH/Q000009 http://purl.bioontology.org/ontology/MESH/Q000031 http://purl.bioontology.org/ontology/MESH/Q000032 http://purl.bioontology.org/ontology/MESH/Q000037 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000302 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000592 http://purl.bioontology.org/ontology/MESH/Q000737 http://purl.bioontology.org/ontology/MESH/Q000819 http://purl.bioontology.org/ontology/MESH/Q000502 http://purl.bioontology.org/ontology/MESH/Q000506 http://purl.bioontology.org/ontology/MESH/Q000187 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000633 http://purl.bioontology.org/ontology/MESH/Q000600 |
|
Inverse of RB |
9013-56-3 |
|
Inverse of RO | ||
Machine permutation |
1970; for FACTOR XIII TRANSAMIDASE use PROTEIN-GLUTAMINE GAMMA-GLUTAMYLTRANSFERASE (1990-2001) |
|
Mapped from |
http://purl.bioontology.org/ontology/MESH/C050909 http://purl.bioontology.org/ontology/MESH/C586540 http://purl.bioontology.org/ontology/MESH/C054380 http://purl.bioontology.org/ontology/MESH/C493000 |
|
MDA |
19990101 |
|
MMR |
20190530 |
|
MN |
D23.119.475 D12.776.124.125.475 D08.622.505 D12.776.811.243.505 |
|
notation |
D005176 |
|
prefLabel |
Factor XIII |
|
TERMUI |
T015852 T000913583 T015853 T015856 T015855 T015857 T015854 T000913582 T015851 T033984 |
|
TH |
NLM (1990) UNK (19XX) NLM (1998) NLM (1964) NLM (2018) |
|
tui |
T116 T126 T121 |
|
subClassOf |