loading...| Preferred Name |
persistent fetal circulation syndrome |
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| Synonyms |
Persistent fetal circulation Persistent fetal circulation (disorder) persistent pulmonary hypertension of the newborn Persistent Fetal Circulation Syndrome Persistent pulmonary hypertension of the newborn (disorder) Persistent fetal circulation syndrome (disorder) congenital alveolar capillary dysplasia with misalignment of pulmonary veins Fetal circulation PPHN persistent fetal circulation persistent foetal circulation persistent fetal circulation syndrome |
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| Definitions |
Editor note: consider relationship to MONDO:0009934 A syndrome of persistent PULMONARY HYPERTENSION in the newborn infant (INFANT, NEWBORN) without demonstrable HEART DISEASES. This neonatal condition can be caused by severe pulmonary vasoconstriction (reactive type), hypertrophy of pulmonary arterial muscle (hypertrophic type), or abnormally developed pulmonary arterioles (hypoplastic type). The newborn patient exhibits CYANOSIS and ACIDOSIS due to the persistence of fetal circulatory pattern of right-to-left shunting of blood through a patent ductus arteriosus (DUCTUS ARTERIOSUS, PATENT) and at times a patent foramen ovale (FORAMEN OVALE, PATENT). A cardiopulmonary disorder characterized by systemic arterial hypoxemia secondary to pulmonary hypertension and extrapulmonary right to left shunting across the foramen ovale and ductus arteriosus. |
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| ID |
http://www.ebi.ac.uk/efo/EFO_1001103 |
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| comment |
Editor note: consider relationship to MONDO:0009934 |
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| database_cross_reference |
OMIM:617039 OMIM:617035 ICD10:P29.3 MeSH:D010547 SNOMEDCT:35604006 NCIt:C85006 MedDRA:10054726 DOID:13042 SCTID:206597007 NCIT:C85006 SCTID:35604006 SCTID:233815004 MONDO:0022430 MESH:D010547 UMLS:C0031190 |
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| definition |
A syndrome of persistent PULMONARY HYPERTENSION in the newborn infant (INFANT, NEWBORN) without demonstrable HEART DISEASES. This neonatal condition can be caused by severe pulmonary vasoconstriction (reactive type), hypertrophy of pulmonary arterial muscle (hypertrophic type), or abnormally developed pulmonary arterioles (hypoplastic type). The newborn patient exhibits CYANOSIS and ACIDOSIS due to the persistence of fetal circulatory pattern of right-to-left shunting of blood through a patent ductus arteriosus (DUCTUS ARTERIOSUS, PATENT) and at times a patent foramen ovale (FORAMEN OVALE, PATENT). A cardiopulmonary disorder characterized by systemic arterial hypoxemia secondary to pulmonary hypertension and extrapulmonary right to left shunting across the foramen ovale and ductus arteriosus. |
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| exactMatch |
http://purl.obolibrary.org/obo/NCIT_C85006 http://linkedlifedata.com/resource/umls/id/C0031190 |
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| has_exact_synonym |
Persistent fetal circulation Persistent fetal circulation (disorder) persistent pulmonary hypertension of the newborn Persistent Fetal Circulation Syndrome Persistent pulmonary hypertension of the newborn (disorder) Persistent fetal circulation syndrome (disorder) congenital alveolar capillary dysplasia with misalignment of pulmonary veins Fetal circulation PPHN persistent fetal circulation persistent foetal circulation persistent fetal circulation syndrome |
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| IAO_0000233 | ||
| id |
EFO:1001103 |
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| in_subset | ||
| label |
persistent fetal circulation syndrome |
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| notation |
EFO:1001103 |
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| prefLabel |
persistent fetal circulation syndrome |
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| relatedMatch | ||
| term editor |
Dani Welter |
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| subClassOf |
http://www.ebi.ac.uk/efo/EFO_0010238 |