Preferred Name |
microscopic polyangiitis |
|
Synonyms |
Hypersensitivity angiitis Microscopic polyarteritis Micropolyangiitis MPA microscopic polyarteritis microscopic polyangiitis |
|
Definitions |
A primary systemic vasculitis of small- and some medium-sized vessels. It is characterized by a tropism for kidneys and lungs, positive association with anti-neutrophil cytoplasmic antibodies (ANCA), and a paucity of immunoglobulin deposits in vessel walls. Microscopic polyangiitis (MPA) is an inflammatory, necrotizing, systemic vasculitis that affects predominantly small vessels (i.e. small arteries, arterioles, capillaries, venules) in multiple organs. |
|
ID |
http://www.ebi.ac.uk/efo/EFO_1000784 |
|
closeMatch | ||
database_cross_reference |
MeSH:D055953 MedDRA:10063344 ICD10:M31.7 MESH:D055953 SCTID:239928004 ICD10CM:M31.7 GARD:3652 icd11.foundation:999231798 NCIT:C70549 UMLS:C2347126 MONDO:0019124 Orphanet:727 |
|
definition |
A primary systemic vasculitis of small- and some medium-sized vessels. It is characterized by a tropism for kidneys and lungs, positive association with anti-neutrophil cytoplasmic antibodies (ANCA), and a paucity of immunoglobulin deposits in vessel walls. Microscopic polyangiitis (MPA) is an inflammatory, necrotizing, systemic vasculitis that affects predominantly small vessels (i.e. small arteries, arterioles, capillaries, venules) in multiple organs. |
|
exactMatch |
http://purl.obolibrary.org/obo/Orphanet_727 http://identifiers.org/mesh/D055953 http://identifiers.org/snomedct/239928004 http://purl.bioontology.org/ontology/ICD10CM/M31.7 |
|
has_exact_synonym |
Hypersensitivity angiitis Microscopic polyarteritis Micropolyangiitis MPA microscopic polyarteritis microscopic polyangiitis |
|
IAO_0000233 | ||
id |
EFO:1000784 |
|
in_subset |
http://purl.obolibrary.org/obo/mondo#ordo_disease http://purl.obolibrary.org/obo/mondo#rare http://purl.obolibrary.org/obo/mondo#nord_rare http://purl.obolibrary.org/obo/mondo#orphanet_rare |
|
label |
microscopic polyangiitis |
|
notation |
EFO:1000784 |
|
prefLabel |
microscopic polyangiitis |
|
see also |
https://rarediseases.info.nih.gov/diseases/3652/microscopic-polyangiitis |
|
term editor |
Sirarat Sarntivijai |
|
excluded_subClassOf | ||
subClassOf |