Experimental Factor Ontology

Last uploaded: May 15, 2024
Preferred Name

microscopic polyangiitis

Synonyms

Hypersensitivity angiitis

Microscopic polyarteritis

Micropolyangiitis

MPA

microscopic polyarteritis

microscopic polyangiitis

Definitions

A primary systemic vasculitis of small- and some medium-sized vessels. It is characterized by a tropism for kidneys and lungs, positive association with anti-neutrophil cytoplasmic antibodies (ANCA), and a paucity of immunoglobulin deposits in vessel walls. Microscopic polyangiitis (MPA) is an inflammatory, necrotizing, systemic vasculitis that affects predominantly small vessels (i.e. small arteries, arterioles, capillaries, venules) in multiple organs.

ID

http://www.ebi.ac.uk/efo/EFO_1000784

closeMatch

http://identifiers.org/meddra/10063344

database_cross_reference

MeSH:D055953

MedDRA:10063344

ICD10:M31.7

MESH:D055953

SCTID:239928004

ICD10CM:M31.7

GARD:3652

icd11.foundation:999231798

NCIT:C70549

UMLS:C2347126

MONDO:0019124

Orphanet:727

definition

A primary systemic vasculitis of small- and some medium-sized vessels. It is characterized by a tropism for kidneys and lungs, positive association with anti-neutrophil cytoplasmic antibodies (ANCA), and a paucity of immunoglobulin deposits in vessel walls.

Microscopic polyangiitis (MPA) is an inflammatory, necrotizing, systemic vasculitis that affects predominantly small vessels (i.e. small arteries, arterioles, capillaries, venules) in multiple organs.

exactMatch

http://purl.obolibrary.org/obo/Orphanet_727

http://identifiers.org/mesh/D055953

http://identifiers.org/snomedct/239928004

http://purl.bioontology.org/ontology/ICD10CM/M31.7

http://purl.obolibrary.org/obo/NCIT_C70549

http://linkedlifedata.com/resource/umls/id/C2347126

has_exact_synonym

Hypersensitivity angiitis

Microscopic polyarteritis

Micropolyangiitis

MPA

microscopic polyarteritis

microscopic polyangiitis

IAO_0000233

https://github.com/monarch-initiative/mondo/issues/5261

id

EFO:1000784

in_subset

http://purl.obolibrary.org/obo/mondo#ordo_disease

http://purl.obolibrary.org/obo/mondo#rare

http://purl.obolibrary.org/obo/mondo#nord_rare

http://purl.obolibrary.org/obo/mondo#orphanet_rare

http://purl.obolibrary.org/obo/mondo#otar

http://purl.obolibrary.org/obo/mondo#gard_rare

label

microscopic polyangiitis

notation

EFO:1000784

prefLabel

microscopic polyangiitis

see also

https://rarediseases.info.nih.gov/diseases/3652/microscopic-polyangiitis

term editor

Sirarat Sarntivijai

excluded_subClassOf

http://purl.obolibrary.org/obo/MONDO_0019724

subClassOf

http://purl.obolibrary.org/obo/MONDO_0015492

http://www.ebi.ac.uk/efo/EFO_0009011

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