Preferred Name

acute hemorrhagic leukoencephalitis

Synonyms

Ahl

AHLE

AHL

acute haemorrhagic leucoencephalitis of Weston Hurst

acute hemorrhagic encephalomyelitis

acute necrotizing hemorrhagic leukoencephalitis

acute hemorrhagic leukoencephalitis

Weston-Hurst syndrome

Definitions

Acute hemorrhagic leukoencephalitis(AHL) is a veryrareform of acute disseminated encephalomyelitis that usuallyresults indeath. It is characterized by a brief but intense attack of inflammation in the brain and spinal cord that damages the myelin -- the protective covering of the nerve fibers. It may also cause bleeding in the brain, leading to damage of the white matter. Symptoms usually come on quickly, beginning with symptoms such as fever, neck stiffness, fatigue, headache, nausea vomiting,seizures, and coma.AHL has a very poor prognosis, with rapid deterioration and death usually occurring within days to one week after onset of symptoms because of severe inflammation in the brain. Although the exact cause is unclear,AHL usually followsaviral infection, or less often, vaccination for measles, mumps, or rubella. Some researchers think that an infection or vaccination can initiate an autoimmune process in the body thus leading to AHL.

ID

http://purl.obolibrary.org/obo/MONDO_0011716

altLabel

Ahl

AHLE

AHL

acute haemorrhagic leucoencephalitis of Weston Hurst

acute hemorrhagic encephalomyelitis

acute necrotizing hemorrhagic leukoencephalitis

acute hemorrhagic leukoencephalitis

Weston-Hurst syndrome

definition

Acute hemorrhagic leukoencephalitis(AHL) is a veryrareform of acute disseminated encephalomyelitis that usuallyresults indeath. It is characterized by a brief but intense attack of inflammation in the brain and spinal cord that damages the myelin -- the protective covering of the nerve fibers. It may also cause bleeding in the brain, leading to damage of the white matter. Symptoms usually come on quickly, beginning with symptoms such as fever, neck stiffness, fatigue, headache, nausea vomiting,seizures, and coma.AHL has a very poor prognosis, with rapid deterioration and death usually occurring within days to one week after onset of symptoms because of severe inflammation in the brain. Although the exact cause is unclear,AHL usually followsaviral infection, or less often, vaccination for measles, mumps, or rubella. Some researchers think that an infection or vaccination can initiate an autoimmune process in the body thus leading to AHL.

has_exact_synonym

AHL

acute haemorrhagic leucoencephalitis of Weston Hurst

acute hemorrhagic encephalomyelitis

acute necrotizing hemorrhagic leukoencephalitis

acute hemorrhagic leukoencephalitis

Weston-Hurst syndrome

has_related_synonym

Ahl

AHLE

label

acute hemorrhagic leukoencephalitis

prefixIRI

MONDO:0011716

prefLabel

acute hemorrhagic leukoencephalitis

seeAlso

https://rarediseases.info.nih.gov/diseases/8629/acute-hemorrhagic-leukoencephalitis

textual definition

Acute hemorrhagic leukoencephalitis(AHL) is a veryrareform of acute disseminated encephalomyelitis that usuallyresults indeath. It is characterized by a brief but intense attack of inflammation in the brain and spinal cord that damages the myelin -- the protective covering of the nerve fibers. It may also cause bleeding in the brain, leading to damage of the white matter. Symptoms usually come on quickly, beginning with symptoms such as fever, neck stiffness, fatigue, headache, nausea vomiting,seizures, and coma.AHL has a very poor prognosis, with rapid deterioration and death usually occurring within days to one week after onset of symptoms because of severe inflammation in the brain. Although the exact cause is unclear,AHL usually followsaviral infection, or less often, vaccination for measles, mumps, or rubella. Some researchers think that an infection or vaccination can initiate an autoimmune process in the body thus leading to AHL.

subClassOf

http://purl.obolibrary.org/obo/MONDO_0003337

http://purl.obolibrary.org/obo/MONDO_0019383

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