Preferred Name |
alveolar rhabdomyosarcoma |
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Synonyms |
pediatric alveolar rhabdomyosarcoma arms alveolar childhood rhabdomyosarcoma rhabdomyosarcoma type 2 rhabdomyosarcoma 2, alveolar, somatic mutation alveolar rhabdomyosarcoma (morphologic abnormality) alveolar rhabdomyosarcoma (disease) alveolar rhabdomyosarcoma rhabdomyosarcoma, alveolar, somatic mutation monomorphous round cell rhabdomyosarcoma rhabdomyosarcoma, alveolar rhabdomyosarcoma alveolar RMS2 rhabdomyosarcoma 2 |
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Definitions |
A rapidly growing malignant mesenchymal neoplasm. It is characterized by the presence of round cells with myoblastic differentiation and a fibrovascular stroma resembling an alveolar growth pattern. The tumor usually presents in the extremities. |
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ID |
http://purl.obolibrary.org/obo/MONDO_0009994 |
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has_exact_synonym |
pediatric alveolar rhabdomyosarcoma arms alveolar childhood rhabdomyosarcoma rhabdomyosarcoma type 2 rhabdomyosarcoma 2, alveolar, somatic mutation alveolar rhabdomyosarcoma (morphologic abnormality) alveolar rhabdomyosarcoma (disease) alveolar rhabdomyosarcoma rhabdomyosarcoma, alveolar, somatic mutation monomorphous round cell rhabdomyosarcoma |
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has_related_synonym |
rhabdomyosarcoma, alveolar rhabdomyosarcoma alveolar RMS2 rhabdomyosarcoma 2 |
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IAO_0000233 | ||
IAO_0000589 |
alveolar rhabdomyosarcoma (disease) |
|
label |
alveolar rhabdomyosarcoma |
|
prefixIRI |
MONDO:0009994 |
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prefLabel |
alveolar rhabdomyosarcoma |
|
textual definition |
A rapidly growing malignant mesenchymal neoplasm. It is characterized by the presence of round cells with myoblastic differentiation and a fibrovascular stroma resembling an alveolar growth pattern. The tumor usually presents in the extremities. |
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subClassOf |