Preferred Name |
acrokeratosis verruciformis |
|
Synonyms |
AKV of Hopf Hopf disease acrokeratosis verruciformis acrokeratosis verruciformis of Hopf AKV |
|
Definitions |
A rare genetic skin keratinization disorder with an autosomal dominant mode of inheritance. It is characterized by numerous flesh-colored warty papules on the back of the hands, medial aspect of the feet, knees, and elbows. |
|
ID |
http://purl.obolibrary.org/obo/MONDO_0007048 |
|
has_exact_synonym |
AKV of Hopf Hopf disease acrokeratosis verruciformis acrokeratosis verruciformis of Hopf |
|
has_related_synonym |
AKV |
|
label |
acrokeratosis verruciformis |
|
prefixIRI |
MONDO:0007048 |
|
prefLabel |
acrokeratosis verruciformis |
|
textual definition |
A rare genetic skin keratinization disorder with an autosomal dominant mode of inheritance. It is characterized by numerous flesh-colored warty papules on the back of the hands, medial aspect of the feet, knees, and elbows. |
|
subClassOf |