Preferred Name

acrokeratosis verruciformis

Synonyms

AKV of Hopf

Hopf disease

acrokeratosis verruciformis

acrokeratosis verruciformis of Hopf

AKV

Definitions

A rare genetic skin keratinization disorder with an autosomal dominant mode of inheritance. It is characterized by numerous flesh-colored warty papules on the back of the hands, medial aspect of the feet, knees, and elbows.

ID

http://purl.obolibrary.org/obo/MONDO_0007048

has_exact_synonym

AKV of Hopf

Hopf disease

acrokeratosis verruciformis

acrokeratosis verruciformis of Hopf

has_related_synonym

AKV

label

acrokeratosis verruciformis

prefixIRI

MONDO:0007048

prefLabel

acrokeratosis verruciformis

textual definition

A rare genetic skin keratinization disorder with an autosomal dominant mode of inheritance. It is characterized by numerous flesh-colored warty papules on the back of the hands, medial aspect of the feet, knees, and elbows.

subClassOf

http://purl.obolibrary.org/obo/MONDO_0019271

http://purl.obolibrary.org/obo/MONDO_0006566

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